Faculty Collaboration Database

Embryonal rhabdomyosarcoma of the ampulla of Vater with long-term survival following pancreaticoduodenectomy. J Pediatr Surg 1990 Dec;25(12):1256-8

Date

12/01/1990

Pubmed ID

2286899

DOI

10.1016/0022-3468(90)90523-c

Scopus ID

2-s2.0-0025681944 (requires institutional sign-in at Scopus site)   29 Citations

Abstract

Rhabdomyosarcoma of the biliary tree is a rare cause of biliary tract obstruction in childhood. A 3-year-old child is reported here after presenting with obstructive jaundice secondary to an embryonal rhabdomyosarcoma of the ampulla of Vater. He underwent pancreaticoduodenectomy followed by adjuvant chemotherapy and irradiation. He is now well and free of disease 5 years following treatment. This child appears to be the first long-term survivor who has required pancreaticoduodenal resection for this lesion.

Author List

Caty MG, Oldham KT, Prochownik EV

MESH terms used to index this publication - Major topics in bold

Ampulla of Vater
Child, Preschool
Combined Modality Therapy
Common Bile Duct Neoplasms
Duodenum
Humans
Male
Pancreatectomy
Prognosis
Rhabdomyosarcoma