Primary mesenteric angiosarcoma in a child with associated lymphangiectasia: a case report. Pediatr Dev Pathol 2008;11(6):482-6
Date
01/16/2009Pubmed ID
19143455DOI
10.2350/08-03-0438.1Scopus ID
2-s2.0-58449111321 (requires institutional sign-in at Scopus site) 6 CitationsAbstract
Angiosarcomas are rare tumors in children, usually occurring in soft tissue and liver. By contrast, angiosarcoma in adults usually occurs in the extremities in conjunction with lymphedema. Mesenteric angiosarcoma has only rarely been reported. When angiosarcomas arise in this location, they usually represent a 2nd malignancy following Hodgkin's lymphoma. We report a child who presented to the emergency room with an acute abdomen and underwent emergency surgery for a mesenteric angiosarcoma with associated lymphangiectasia of the bowel and mesentery. A brief review of the literature and the nomenclature of these unusual tumors are discussed.
Author List
Castro EC, Galambos C, Shaw PH, Ranganathan SAuthor
Peter H. Shaw MD Associate Professor in the Pediatrics department at Medical College of WisconsinMESH terms used to index this publication - Major topics in bold
Antineoplastic Combined Chemotherapy ProtocolsBiomarkers, Tumor
Child
Combined Modality Therapy
Fatal Outcome
Female
Hemangiosarcoma
Humans
Lymphangiectasis, Intestinal
Mesentery
Peritoneal Neoplasms
