Medical College of Wisconsin
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Orbital histiocytic sarcoma in a 2-year-old child. Ophthalmic Plast Reconstr Surg 2014;30(6):e143-5

Date

05/09/2014

Pubmed ID

24807797

Pubmed Central ID

PMC4222992

DOI

10.1097/IOP.0b013e3182a74e3b

Scopus ID

2-s2.0-84926214495 (requires institutional sign-in at Scopus site)   5 Citations

Abstract

Histiocytic sarcoma (HS) is an exceedingly rare hematologic malignancy that typically presents in the skin, gastrointestinal tract, and lymph nodes. Few cases of HS have been reported in the head and neck. This study describes the case of a 2-year-old girl presenting with 2 weeks of left lower eyelid swelling. Diagnostic testing and biopsy revealed a large inferior orbital mass causing severe bony destruction with extension into the sinuses. Pathologic analysis revealed classic features of HS. To the best of knowledge, no previous case of HS occurring in the orbit of a child has been reported. This study presents an exceedingly rare case of HS in a young child presenting with eyelid swelling. In addition, this case report is in compliance with HIPAA regulations.

Author List

Aakalu VK, Patel RM, Lim J, Setabutr P

Author

Vinay Kumar Aakalu MPH, MD Chair, Professor in the Ophthalmology department at Medical College of Wisconsin




MESH terms used to index this publication - Major topics in bold

Biopsy
Child, Preschool
Female
Histiocytic Sarcoma
Humans
Orbital Neoplasms
Tomography, X-Ray Computed