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Preliminary reliability and validity of a battery for assessing functional skills in children with Sturge-Weber syndrome. Childs Nerv Syst 2014 Dec;30(12):2027-36

Date

10/27/2014

Pubmed ID

25344741

Pubmed Central ID

PMC4276129

DOI

10.1007/s00381-014-2573-6

Scopus ID

2-s2.0-84922004836 (requires institutional sign-in at Scopus site)   7 Citations

Abstract

PURPOSE: The purpose of this study was to evaluate inter-rater reliability and validity of a proposed functional outcome battery for clinical trials in children with Sturge-Weber syndrome (SWS).

METHODS: Ten children were evaluated twice on the same day using a series of functional outcome measures selected for sensitivity to the range of age and function of children with SWS: Modified Rankin Scale, Pediatric Evaluation of Disability Index, Modified House Functional Classification, and a modified version of the Erhardt Developmental Prehension Assessment. Inter-rater reliability was calculated, and criterion validity was explored through correlations with the Sturge-Weber Syndrome-Neurological Rating Score (SWS-NRS).

RESULTS: Inter-rater reliability was high across all measures. Correlations were identified between the SWS-NRS and the study measures.

CONCLUSIONS: The proposed battery of functional outcome measures captures child's functioning at the levels of impairment, activity and participation and is robust to evaluation by different raters and across sessions on the same day. This battery is expected to be sensitive to treatment-related changes in qualitative patterns of hand use, functional skills, and/or change in independence in daily living.

Author List

Reidy TG, Suskauer SJ, Bachur CD, McCulloch CE, Comi AM

Author

Catherine Bachur MD, MA Maternal Fetal Medicine Fellow in the Obstetrics and Gynecology department at Medical College of Wisconsin




MESH terms used to index this publication - Major topics in bold

Activities of Daily Living
Child
Child, Preschool
Disability Evaluation
Female
Humans
Infant
Male
Neurologic Examination
Observer Variation
Psychometrics
Reproducibility of Results
Sturge-Weber Syndrome