Medical College of Wisconsin
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Management of a Patient With Tetralogy of Fallot, Congenital Diaphragmatic Hernia, and Complete Left Lung Agenesis. A A Case Rep 2016 Jul 01;7(1):16-20

Date

06/04/2016

Pubmed ID

27258177

DOI

10.1213/XAA.0000000000000328

Scopus ID

2-s2.0-85021851271 (requires institutional sign-in at Scopus site)   3 Citations

Abstract

We describe the rare case of an infant with congenital diaphragmatic hernia, unilateral lung agenesis, and unpalliated single-ventricle physiology. Infants with congenital diaphragmatic hernia and parallel circulation are at risk for maldistribution of systemic and pulmonary blood flow. Optimal perioperative management should include an assessment of the ratio of pulmonary to systemic blood flow (Qp:Qs). Traditionally, arterial and systemic venous oxygen (SvO2) saturations are needed to calculate Qp:Qs. However, in this case, SvO2 measurement was not feasible. On the basis of a previously described relationship, we used 2-site near-infrared spectroscopy to calculate a near-infrared spectroscopy-derived SvO2, which was then used to estimate Qp:Qs and guide goal-directed interventions.

Author List

Labovsky K, Hoffman G, Scott J

Authors

George M. Hoffman MD Chief, Professor in the Anesthesiology department at Medical College of Wisconsin
Kristen Labovsky MD Assistant Professor in the Anesthesiology department at Medical College of Wisconsin
John P. Scott MD Professor in the Anesthesiology department at Medical College of Wisconsin




MESH terms used to index this publication - Major topics in bold

Abnormalities, Multiple
Disease Management
Female
Hernias, Diaphragmatic, Congenital
Humans
Infant, Newborn
Lung
Lung Diseases
Tetralogy of Fallot