Medical College of Wisconsin
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Publications indexed to the term Acyl-CoA Dehydrogenase, Long-Chain

FacultyTitle
1Structural basis for expanded substrate specificities of human long chain acyl-CoA dehydrogenase and related acyl-CoA dehydrogenases. (Narayanan B, Xia C, McAndrew R, Shen AL, Kim JP) Sci Rep 2024 Jun 05;14(1):12976       5 Citations
1The protein partners of GTP cyclohydrolase I in rat organs. (Du J, Teng RJ, Lawrence M, Guan T, Xu H, Ge Y, Shi Y) PLoS One 2012;7(3):e33991       13 Citations
1Compared effects of missense mutations in Very-Long-Chain Acyl-CoA Dehydrogenase deficiency: Combined analysis by structural, functional and pharmacological approaches. (Gobin-Limballe S, McAndrew RP, Djouadi F, Kim JJ, Bastin J) Biochim Biophys Acta 2010 May;1802(5):478-84       35 Citations
1Structural basis for substrate fatty acyl chain specificity: crystal structure of human very-long-chain acyl-CoA dehydrogenase. (McAndrew RP, Wang Y, Mohsen AW, He M, Vockley J, Kim JJ) J Biol Chem 2008 Apr 04;283(14):9435-43       95 Citations
1Evaluation of liver fatty acid oxidation in the leptin-deficient obese mouse. (Brix AE, Elgavish A, Nagy TR, Gower BA, Rhead WJ, Wood PA) Mol Genet Metab 2002 Mar;75(3):219-26       33 Citations
1Gestational, pathologic and biochemical differences between very long-chain acyl-CoA dehydrogenase deficiency and long-chain acyl-CoA dehydrogenase deficiency in the mouse. (Cox KB, Hamm DA, Millington DS, Matern D, Vockley J, Rinaldo P, Pinkert CA, Rhead WJ, Lindsey JR, Wood PA) Hum Mol Genet 2001 Sep 15;10(19):2069-77       114 Citations
1Targeted disruption of mouse long-chain acyl-CoA dehydrogenase gene reveals crucial roles for fatty acid oxidation. (Kurtz DM, Rinaldo P, Rhead WJ, Tian L, Millington DS, Vockley J, Hamm DA, Brix AE, Lindsey JR, Pinkert CA, O'Brien WE, Wood PA) Proc Natl Acad Sci U S A 1998 Dec 22;95(26):15592-7       215 Citations
1Analysis of carnitine esters by radio-high performance liquid chromatography in cultured skin fibroblasts from patients with mitochondrial fatty acid oxidation disorders. (Schmidt-Sommerfeld E, Bobrowski PJ, Penn D, Rhead WJ, Wanders RJ, Bennett MJ) Pediatr Res 1998 Aug;44(2):210-4       17 Citations
1Cloning of human very-long-chain acyl-coenzyme A dehydrogenase and molecular characterization of its deficiency in two patients. (Aoyama T, Souri M, Ueno I, Kamijo T, Yamaguchi S, Rhead WJ, Tanaka K, Hashimoto T) Am J Hum Genet 1995 Aug;57(2):273-83       76 Citations
1Purification of human very-long-chain acyl-coenzyme A dehydrogenase and characterization of its deficiency in seven patients. (Aoyama T, Souri M, Ushikubo S, Kamijo T, Yamaguchi S, Kelley RI, Rhead WJ, Uetake K, Tanaka K, Hashimoto T) J Clin Invest 1995 Jun;95(6):2465-73       160 Citations
1Evidence for intermediate channeling in mitochondrial beta-oxidation. (Nada MA, Rhead WJ, Sprecher H, Schulz H, Roe CR) J Biol Chem 1995 Jan 13;270(2):530-5       101 Citations
1A novel disease with deficiency of mitochondrial very-long-chain acyl-CoA dehydrogenase. (Aoyama T, Uchida Y, Kelley RI, Marble M, Hofman K, Tonsgard JH, Rhead WJ, Hashimoto T) Biochem Biophys Res Commun 1993 Mar 31;191(3):1369-72       151 Citations
1Defect in fatty acid oxidation: laboratory and pathologic findings in a patient. (Tonsgard JH, Stephens JK, Rhead WJ, Penn D, Horwitz AL, Kirschner BS, Whitington PF, Berger S, Tripp ME) Pediatr Neurol 1991;7(2):125-30       6 Citations
1Long-chain acyl-coenzyme A dehydrogenase deficiency: biochemical studies in fibroblasts from three patients. (Amendt BA, Moon A, Teel L, Rhead WJ) Pediatr Res 1988 Jun;23(6):603-5       18 Citations
1Complementation analysis of fatty acid oxidation disorders. (Moon A, Rhead WJ) J Clin Invest 1987 Jan;79(1):59-64       92 Citations