Orthotopic heart transplantation in two infants with histiocytoid cardiomyopathy and left ventricular non-compaction. Pediatr Transplant 2013 Nov;17(7):E165-7
Date
10/09/2013Pubmed ID
24099092DOI
10.1111/petr.12141Scopus ID
2-s2.0-84885395108 (requires institutional sign-in at Scopus site) 5 CitationsAbstract
HC is a rare cause of congestive heart failure that typically presents with malignant ventricular arrhythmias in infants, often requiring urgent intervention. Successful heart transplantation in a patient with HC has only been reported once (J Heart Lung Transplant 2004: 23: 902). The combination of HC with concurrent LVNC has only been described three times (Int J Legal Med 2009: 123: 47; Hum Pathol 2005: 36: 403; Pediatr Dev Pathol 2012: 15: 397). We report two rare cases of HC with LVNC in two infants presenting with cardiogenic shock, one requiring ECMO support who was successfully bridged to orthotopic heart transplantation with a Berlin Heart LVAD.
Author List
Siehr SL, Bernstein D, Yeh J, Berry GJ, Rosenthal DN, Hollander SAAuthor
Stephanie S. Handler MD Associate Professor in the Pediatrics department at Medical College of WisconsinMESH terms used to index this publication - Major topics in bold
CardiomyopathiesCardiomyopathy, Dilated
Electron Transport Complex III
Extracorporeal Membrane Oxygenation
Female
Heart
Heart Failure
Heart Transplantation
Heart Ventricles
Heart-Assist Devices
Humans
Infant
Male
Shock, Cardiogenic
Treatment Outcome
