Medical College of Wisconsin
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Cranio-orbital-temporal neurofibromatosis: are we treating the whole problem? J Craniofac Surg 1998 Nov;9(6):529-35

Date

02/25/1999

Pubmed ID

10029765

DOI

10.1097/00001665-199811000-00007

Scopus ID

2-s2.0-0031762722 (requires institutional sign-in at Scopus site)   28 Citations

Abstract

Cranio-orbital-temporal neurofibromatosis is an uncommon subtype of neurofibromatosis 1 characterized by pulsatile exophthalmos, orbital neurofibromas, sphenoid wing dysplasia, expansion of the temporal fossa, and herniation of the temporal lobe into the orbit. The cause of the sphenoid wing dysplasia is uncertain. Reconstruction of the sphenoid defect, separating the orbit and cranial vault, has been problematic because of resorption of bone grafts. This reports illustrates one potential cause of the sphenoid defect and a possible cause of the bone graft resorption.

Author List

Havlik RJ, Boaz J

Author

Robert Havlik MD Chair, Professor in the Plastic Surgery department at Medical College of Wisconsin




MESH terms used to index this publication - Major topics in bold

Bone Resorption
Bone Transplantation
Cerebrospinal Fluid Shunts
Craniotomy
Female
Humans
Infant
Intracranial Hypertension
Neoplasm Recurrence, Local
Neurofibromatosis 1
Orbit
Skull Neoplasms
Sphenoid Bone
Tomography, X-Ray Computed