Multivalvular Replacement and Ventricular Arrhythmias in a Female Child With Congenital Polyvalvular Disease. World J Pediatr Congenit Heart Surg 2014 Jul;5(3):463-6
Date
06/25/2014Pubmed ID
24958053DOI
10.1177/2150135113516983Scopus ID
2-s2.0-84993683814 (requires institutional sign-in at Scopus site) 1 CitationAbstract
We report the clinical course of a female child with a normal karyotype and chromosomal microarray who presented as an infant with clinical findings consistent with congenital polyvalvular disease (CPVD). This clinical entity describes patients with multiple congenitally dysplastic valves, often showing nodular or cystic malformation in at least two cardiac valves. This patient then developed medically refractory multifocal ventricular arrhythmia and required radiofrequency ablation at seven months of age. She had good tachycardia control but became symptomatic with right heart failure related to progressive tricuspid, pulmonary, and mitral valve dysfunction necessitating multivalvular replacement at 21 months of age.
Author List
Goot BH, Jaggers J, Anagnost MR, Collins KKAuthor
Ben Goot MD Associate Professor in the Pediatrics department at Medical College of WisconsinMESH terms used to index this publication - Major topics in bold
Aortic ValveEchocardiography
Electrocardiography
Female
Follow-Up Studies
Heart Valve Diseases
Heart Valve Prosthesis Implantation
Humans
Infant, Newborn
Mitral Valve
Tachycardia, Ventricular
