Monomelic amyotrophy with late progression. Neuromuscul Disord 2001 Apr;11(3):305-8
Date
04/12/2001Pubmed ID
11297947DOI
10.1016/s0960-8966(00)00202-9Scopus ID
2-s2.0-0035072042 (requires institutional sign-in at Scopus site) 18 CitationsAbstract
Monomelic amyotrophy is a sporadic juvenile-onset disease that presents with gradual onset of weakness and atrophy in the hand muscles unilaterally. Generally, this disease is considered a 'benign' and non-progressive motor neuron disease, which stabilizes within five years of onset. We discuss a case that illustrates that monomelic amyotrophy may rarely exhibit late clinical progression to the lower extremities after a prolonged period of disease stability.
Author List
Rowin J, Meriggioli MN, Cochran EJAuthor
Elizabeth J. Cochran MD Adjunct Professor in the Pathology department at Medical College of WisconsinMESH terms used to index this publication - Major topics in bold
Age of OnsetBiopsy
Disease Progression
Humans
Leg
Male
Middle Aged
Muscle, Skeletal
Muscular Atrophy, Spinal
Neural Conduction
Predictive Value of Tests