A composite pheochromocytoma/ganglioneuroblastoma of the adrenal gland. Pediatr Blood Cancer 2010 Jul 01;54(7):1032-4
Date
02/18/2010Pubmed ID
20162688DOI
10.1002/pbc.22436Scopus ID
2-s2.0-77951755386 (requires institutional sign-in at Scopus site) 13 CitationsAbstract
A 9-year-old female presented with a large abdominal mass. At surgery, the mass was noted to arise from the right adrenal gland. As the mass was manipulated, the patient developed severe hypertension. The final diagnosis was a cystic composite-pheochromocytoma/ganglioneuroblastoma. This compound adrenal tumor is only the fourth case reported in a child. Because composite pheochromocytomas are rare in the pediatric population, the management, optimal surveillance schedule and outcomes have not been characterized.
Author List
Thiel EL, Trost BA, Tower RLAuthors
Elizabeth Thiel MD Associate Professor in the Medicine department at Medical College of WisconsinRichard L. Tower MD Professor in the Pediatrics department at Medical College of Wisconsin
MESH terms used to index this publication - Major topics in bold
Adrenal Gland NeoplasmsChild
Female
Ganglioneuroblastoma
Humans
Immunohistochemistry
Neoplasms, Multiple Primary
Pheochromocytoma