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A composite pheochromocytoma/ganglioneuroblastoma of the adrenal gland. Pediatr Blood Cancer 2010 Jul 01;54(7):1032-4

Date

02/18/2010

Pubmed ID

20162688

DOI

10.1002/pbc.22436

Scopus ID

2-s2.0-77951755386 (requires institutional sign-in at Scopus site)   13 Citations

Abstract

A 9-year-old female presented with a large abdominal mass. At surgery, the mass was noted to arise from the right adrenal gland. As the mass was manipulated, the patient developed severe hypertension. The final diagnosis was a cystic composite-pheochromocytoma/ganglioneuroblastoma. This compound adrenal tumor is only the fourth case reported in a child. Because composite pheochromocytomas are rare in the pediatric population, the management, optimal surveillance schedule and outcomes have not been characterized.

Author List

Thiel EL, Trost BA, Tower RL

Authors

Elizabeth Thiel MD Associate Professor in the Medicine department at Medical College of Wisconsin
Richard L. Tower MD Professor in the Pediatrics department at Medical College of Wisconsin




MESH terms used to index this publication - Major topics in bold

Adrenal Gland Neoplasms
Child
Female
Ganglioneuroblastoma
Humans
Immunohistochemistry
Neoplasms, Multiple Primary
Pheochromocytoma