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Liver transplantation for a hilar inflammatory myofibroblastic tumor. Pediatr Transplant 2004 Oct;8(5):517-21

Date

09/16/2004

Pubmed ID

15367291

DOI

10.1111/j.1399-3046.2004.00206.x

Scopus ID

2-s2.0-4644312265 (requires institutional sign-in at Scopus site)   16 Citations

Abstract

A 7-yr-old boy presented with obstructive jaundice secondary to an inflammatory myofibroblastic tumor centered on the hepatic hilum and extending into the liver. The tumor was further complicated by portal vein phlebitis and occlusion. Attempted resection of the tumor with portal vein reconstruction and bilioenteric drainage was unsuccessful and he required urgent orthotopic liver transplantation. In contrast to more peripheral inflammatory myofibroblastic tumors in the liver, hilar lesions are locally aggressive, causing occlusive portal phlebitis and biliary obstruction. Successful management may include the need for liver transplantation.

Author List

Dasgupta D, Guthrie A, McClean P, Davison S, Luntley J, Rajwal S, Lodge JP, Prasad KR, Wyatt JI, Stringer MD

Author

Kondragunta Rajendra Prasad MBBS Professor in the Surgery department at Medical College of Wisconsin




MESH terms used to index this publication - Major topics in bold

Child
Humans
Inflammation
Jaundice, Obstructive
Liver
Liver Neoplasms
Liver Transplantation
Magnetic Resonance Imaging
Male
Neoplasms, Muscle Tissue
Portal Vein
Radiography
Treatment Outcome