Faculty Collaboration Database

Congenital short bowel syndrome with left acheiria: report of one case. Zhonghua Min Guo Xiao Er Ke Yi Xue Hui Za Zhi 1997;38(5):393-5

Date

12/24/1997

Pubmed ID

9401186

Scopus ID

2-s2.0-0031419636 (requires institutional sign-in at Scopus site)   3 Citations

Abstract

A case of congenital short bowel syndrome with left acheiria, hemivertebra and dextrocardia is described. Dilatation of the fetal bowel was observed at the 24th week of gestation during a routine ultrasonic scan of a healthy 23-year-old primigravida from a non-consanguineous marriage. Amniocentesis and chorionic villus sampling were denied. The baby was delivered at 38 weeks of gestational age. After delivery, multiple anomalies were noted: left acheiria, congenital short bowel syndrome (15 cm in length of the ileum), pseudo-obstruction of intestine, dextrocardia, and hemivertebrae. We suspected these abnormalities might be due to a vascular accident or failure of lateralization during the early gestational period. To our knowledge, these combinations have not been reported previously in English literature.

Author List

Lin JH, Chang MH, Teng RJ, Yau KI, Wang TR

Author

Ru-Jeng Teng MD Professor in the Pediatrics department at Medical College of Wisconsin

MESH terms used to index this publication - Major topics in bold

Adult
Arm
Female
Humans
Infant, Newborn
Pregnancy
Short Bowel Syndrome