Congenital short bowel syndrome with left acheiria: report of one case. Zhonghua Min Guo Xiao Er Ke Yi Xue Hui Za Zhi 1997;38(5):393-5
Date
12/24/1997Pubmed ID
9401186Scopus ID
2-s2.0-0031419636 (requires institutional sign-in at Scopus site) 3 CitationsAbstract
A case of congenital short bowel syndrome with left acheiria, hemivertebra and dextrocardia is described. Dilatation of the fetal bowel was observed at the 24th week of gestation during a routine ultrasonic scan of a healthy 23-year-old primigravida from a non-consanguineous marriage. Amniocentesis and chorionic villus sampling were denied. The baby was delivered at 38 weeks of gestational age. After delivery, multiple anomalies were noted: left acheiria, congenital short bowel syndrome (15 cm in length of the ileum), pseudo-obstruction of intestine, dextrocardia, and hemivertebrae. We suspected these abnormalities might be due to a vascular accident or failure of lateralization during the early gestational period. To our knowledge, these combinations have not been reported previously in English literature.
Author List
Lin JH, Chang MH, Teng RJ, Yau KI, Wang TRAuthor
Ru-Jeng Teng MD Professor in the Pediatrics department at Medical College of WisconsinMESH terms used to index this publication - Major topics in bold
AdultArm
Female
Humans
Infant, Newborn
Pregnancy
Short Bowel Syndrome