Medical College of Wisconsin
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Congenital short bowel syndrome with left acheiria: report of one case. Zhonghua Min Guo Xiao Er Ke Yi Xue Hui Za Zhi 1997 Sep-Oct;38(5):393-5



Pubmed ID



A case of congenital short bowel syndrome with left acheiria, hemivertebra and dextrocardia is described. Dilatation of the fetal bowel was observed at the 24th week of gestation during a routine ultrasonic scan of a healthy 23-year-old primigravida from a non-consanguineous marriage. Amniocentesis and chorionic villus sampling were denied. The baby was delivered at 38 weeks of gestational age. After delivery, multiple anomalies were noted: left acheiria, congenital short bowel syndrome (15 cm in length of the ileum), pseudo-obstruction of intestine, dextrocardia, and hemivertebrae. We suspected these abnormalities might be due to a vascular accident or failure of lateralization during the early gestational period. To our knowledge, these combinations have not been reported previously in English literature.

Author List

Lin JH, Chang MH, Teng RJ, Yau KI, Wang TR


Ru-Jeng Teng MD Associate Professor in the Pediatrics department at Medical College of Wisconsin

MESH terms used to index this publication - Major topics in bold

Infant, Newborn
Short Bowel Syndrome
jenkins-FCD Prod-478 d1509cf07a111124a2d122fd3df854cc0b993c00