Colonic adenocarcinoma in a 13-year-old with cystic fibrosis. J Pediatr Surg 2007 Oct;42(10):E1-3
Date
10/10/2007Pubmed ID
17923181DOI
10.1016/j.jpedsurg.2007.07.024Scopus ID
2-s2.0-34848913704 (requires institutional sign-in at Scopus site) 12 CitationsAbstract
The increase in longevity among patients with cystic fibrosis has brought to light comorbidities associated with the disease that are less acutely fatal than its pulmonary manifestations. Modern retrospective analysis has demonstrated an increased risk of gastrointestinal malignancy in patients with cystic fibrosis, with a marked elevation in malignancy rates among patients in their 20s and 30s. Here we report a case of colonic adenocarcinoma presenting as pneumaturia in a 13-year-old patient with cystic fibrosis.
Author List
Ibele AR, Koplin SA, Slaughenhoupt BL, Kryger JV, Friedl A, Lund DPAuthor
John V. Kryger MD Professor in the Urologic Surgery department at Medical College of WisconsinMESH terms used to index this publication - Major topics in bold
AdenocarcinomaAdolescent
Air
Anastomosis, Surgical
Antineoplastic Combined Chemotherapy Protocols
Cecal Neoplasms
Colectomy
Combined Modality Therapy
Cystic Fibrosis
Fluorouracil
Humans
Intestinal Fistula
Leucovorin
Male
Organoplatinum Compounds
Ultrasonography
Urinary Bladder Fistula
Urine