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Type 2 Abernethy malformation presenting as a portal vein-coronary sinus fistula. J Pediatr Surg 2012 May;47(5):E25-31

Date

05/19/2012

Pubmed ID

22595606

DOI

10.1016/j.jpedsurg.2011.12.031

Scopus ID

2-s2.0-84861134308 (requires institutional sign-in at Scopus site)   14 Citations

Abstract

We report the case of a child with Abernethy malformation with an anomalous connection between the portal vein and the coronary sinus. After 30 months of close follow-up, the patient developed hepatoblastoma, a previously documented complication of the Abernethy malformation. This case reports a unique variant of Abernethy malformation and documents the first reported case of hepatoblastoma in a patient with type 2 Abernethy malformation.

Author List

Loomba RS, Telega GW, Gudausky TM

Authors

Todd M. Gudausky MD Associate Professor in the Pediatrics department at Medical College of Wisconsin
Grzegorz W. Telega MD Professor in the Pediatrics department at Medical College of Wisconsin




MESH terms used to index this publication - Major topics in bold

Child, Preschool
Coronary Sinus
Diseases in Twins
Fatal Outcome
Hepatoblastoma
Humans
Infant
Infant, Newborn
Liver Neoplasms
Male
Portal Vein
Vascular Fistula