The neuropathies of vasculitis. Neurol Clin 2013 May;31(2):557-95
Date
05/07/2013Pubmed ID
23642724DOI
10.1016/j.ncl.2013.01.007Scopus ID
2-s2.0-84877140603 (requires institutional sign-in at Scopus site) 38 CitationsAbstract
Vasculitic neuropathy can occur as an isolated entity (nonsystemic vasculitic neuropathy) but more commonly evolves in the setting of primary systemic vasculitides or secondary vasculitides related to infections, drugs, or connective tissue disorders. Vasculitic neuropathies are usually but not always painful and tend to produce sensory motor or sensory symptoms. Patients with purely motor or small-fiber dysfunction are unlikely to have vasculitis. Deficits are typically multifocal or asymmetric, but distal symmetric polyneuropathy occurs uncommonly. Evaluation requires laboratory tests, electrodiagnostic studies, and nerve or nerve/muscle biopsy. This article reviews classification, clinical presentation, diagnostic evaluation, and management of peripheral nerve vasculitis.
Author List
Collins MP, Arnold WD, Kissel JTAuthor
Michael P. Collins MD Professor in the Neurology department at Medical College of WisconsinMESH terms used to index this publication - Major topics in bold
Adrenal Cortex HormonesAged
Biopsy
Electrodiagnosis
Female
Humans
Immunotherapy
Pain
Peripheral Nerves
Peripheral Nervous System Diseases
Vasculitis