Agenesis of the venous duct: two cases of extrahepatic drainage of the umbilical vein and extrahepatic portosystemic shunt with a review of the literature. Cardiol Young 2015 Feb;25(2):208-17
Date
05/23/2014Pubmed ID
24848245DOI
10.1017/S1047951114000729Scopus ID
2-s2.0-84927695223 (requires institutional sign-in at Scopus site) 4 CitationsAbstract
Agenesis of the venous duct is a rare congenital anomaly resulting in abnormal drainage of the umbilical vein into the foetal venous circulation. The clinical presentation and prognosis is variable, and may depend on the specific drainage pathways of the umbilical vein. We present two foetuses with agenesis of the venous duct, both associated with a postnatal portosystemic shunt, but with markedly different postnatal clinical courses. We also review all previously reported cases to better characterise this foetal disorder and the prognosis.
Author List
Loomba RS, Frommelt M, Moe D, Shillingford AJAuthor
David C. Moe MD Associate Professor in the Radiology department at Medical College of WisconsinMESH terms used to index this publication - Major topics in bold
Abnormalities, MultipleAdult
Angiography
Echocardiography
Female
Heart Atria
Hepatic Veins
Humans
Hypertension, Pulmonary
Infant, Newborn
Portal Vein
Pregnancy
Ultrasonography, Prenatal
Umbilical Veins
Vascular Malformations
Vena Cava, Inferior
Young Adult
