Medical College of Wisconsin
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Rare Cause of Infranodal Block. Card Electrophysiol Clin 2016 Dec;8(4):743-745

Date

11/14/2016

Pubmed ID

27837893

DOI

10.1016/j.ccep.2016.07.005

Scopus ID

2-s2.0-84995676505 (requires institutional sign-in at Scopus site)   3 Citations

Abstract

The patient exhibits multiple features suggestive of Timothy syndrome, which is a multisystem autosomal-dominant condition with findings that include prolonged QT interval, hand and foot abnormalities, dysmorphic facial features, and mental retardation. A 2:1 infranodal atrioventricular block may occasionally be seen in the setting of severely prolonged QT interval. Functional nature of atrioventricular block is demonstrated by resumption of 1:1 conduction with changes in heart rate.

Author List

Dhala AA, Singh AK

Author

Anoop K. Singh MD Associate Professor in the Pediatrics department at Medical College of Wisconsin




MESH terms used to index this publication - Major topics in bold

Atrioventricular Block
Autistic Disorder
Electrocardiography
Female
Humans
Infant
Infant, Newborn
Long QT Syndrome
Syndactyly