Inoperable aggressive mesenteric fibromatosis with ureteric fistula. Case report and literature review. Eur J Radiol 2006 Jul;59(1):117-21
Date
02/09/2006Pubmed ID
16464556DOI
10.1016/j.ejrad.2005.12.036Scopus ID
2-s2.0-33745190723 (requires institutional sign-in at Scopus site) 19 CitationsAbstract
The purpose of our report is to illustrate an aggressive case of mesenteric fibromatosis in a 17-year-old girl with a ureteric fistula and to review imaging and pathological features, natural history and treatment options of this disease. Our patient underwent computed tomography that revealed a widespread intra-abdominal mass. The necrotic centre of this mass had a fistulous communication with the right ureter. Fibromatoses represent a spectrum of uncommon benign conditions characterised by proliferating fibrous tissue. The deep intra-abdominal form of mesenteric fibromatosis (MF), one of the rare subtypes of the 'fibromatoses' or 'desmoid tumours', grows rapidly and may become extensive. Surgery provides good results in limited disease and non-surgical modalities in cases of unresectable and residual disease.
Author List
Lath C, Khanna PC, Gadewar SB, Agrawal DAuthor
Dilpesh S. Agrawal MD Assistant Professor in the Medicine department at Medical College of WisconsinMESH terms used to index this publication - Major topics in bold
AdolescentBiopsy
Fatal Outcome
Female
Fibromatosis, Abdominal
Fibromatosis, Aggressive
Humans
Mesentery
Radiography, Interventional
Tomography, X-Ray Computed
Ureteral Diseases
Urinary Fistula
