Faculty Collaboration Database

Aortopulmonary window. Semin Thorac Cardiovasc Surg Pediatr Card Surg Annu 2011;14(1):67-74

Date

03/30/2011

Pubmed ID

21444051

DOI

10.1053/j.pcsu.2011.01.017

Scopus ID

2-s2.0-79953066772 (requires institutional sign-in at Scopus site)   42 Citations

Abstract

Aortopulmonary window is a rare defect caused by failure of fusion of the two opposing conotruncal ridges that are responsible for separating the truncus arteriosus into the aorta and pulmonary artery. Aortopulmonary window may occur as an isolated lesion or it can be associated with other cardiac abnormalities in one third to one half of cases. The most common associated lesions are arch abnormalities, specifically interrupted aortic arch and coarctation of the aorta. Antenatal diagnosis is rare. In the current era, early mortality following repair of simple aortopulmonary window approaches zero and depends on the presence of associated lesions, especially interrupted aortic arch. Long-term outcome should be excellent. Early morbidity includes pulmonary artery stenosis and residual aortopulmonary septal defects. Long-term follow-up is indicated to look for recurrent lesions such as the development of branch pulmonary artery stenosis and arch obstruction.

Author List

Barnes ME, Mitchell ME, Tweddell JS

Author

Michael Edward Mitchell MD Chief, Professor in the Surgery department at Medical College of Wisconsin

MESH terms used to index this publication - Major topics in bold

Aortopulmonary Septal Defect
Cardiac Surgical Procedures
Cardiopulmonary Bypass
Cardiovascular Abnormalities
Female
Follow-Up Studies
Humans
Infant
Infant, Newborn
Male
Rare Diseases
Risk Assessment
Severity of Illness Index
Survival Analysis
Treatment Outcome
Vascular Surgical Procedures