Mesh term Basal Cell Nevus Syndrome
Browse to parent terms:Abnormalities, Multiple
Bone Diseases, Developmental
Carcinoma, Basal Cell
Neoplastic Syndromes, Hereditary
Odontogenic Cysts
Description
Hereditary disorder consisting of multiple basal cell carcinomas, odontogenic keratocysts, and multiple skeletal defects, e.g., frontal and temporoparietal bossing, bifurcated and splayed ribs, kyphoscoliosis, fusion of vertebrae, and cervicothoracic spina bifida. Genetic transmission is autosomal dominant.Search for this term in our Faculty Database
View this term at the NCBI website
