Medical College of Wisconsin
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Robert R. Montgomery MD

Robert R. Montgomery MD profile photo picture

Emeritus Professor

Institution: Medical College of Wisconsin
Department: Pediatrics
Division: Pediatrics Operations

Member of the Cardiovascular Research Center

View Curriculum Vitae

Community Partnerships

  • BloodCenter of Wisconsin
    Great Lakes Hemophilia Foundation
    Children's Hospital of Wisconsin
    Hemophilia and Thrombosis Research Society
    International Society of Thrombosis and Haemophilia
    National Hemophilia Foundation

    • Publications (228)

  • Von Willebrand factor structure and function (Montgomery RR, Flood VH, Haberichter SL) Textbook of Von Willebrand Disease Basic and Clinical Aspects 1 January 2024:23-38 SCOPUS ID: 2-s2.0-85192323441 01/01/2024       3 Citations
  • Molecular diagnosis of von Willebrand disease: The genotype (Christopherson P, Montgomery RR, Flood VH) Textbook of Von Willebrand Disease Basic and Clinical Aspects 1 January 2024:109-114 SCOPUS ID: 2-s2.0-85192305944 01/01/2024    
  • Preface (Federici AB, Berntorp EE, Lillicrap D, Montgomery RR) Textbook of Von Willebrand Disease Basic and Clinical Aspects 1 January 2024:xiii SCOPUS ID: 2-s2.0-85192318820 01/01/2024    
  • Textbook of von Willebrand Disease: Basic and Clinical Aspects (Federici AB, Berntorp EE, Lillicrap D, Montgomery RR) Textbook of Von Willebrand Disease Basic and Clinical Aspects 1 January 2024:1-280 SCOPUS ID: 2-s2.0-85192298029 01/01/2024       1 Citation
  • Characterization of copy-number variants in a large cohort of patients with von Willebrand disease reveals a relationship between disrupted regions and disease type. (Sadler B, Christopherson PA, Perry CL, Bellissimo DB, Haberichter SL, Haller G, Antunes L, Flood VH, Di Paola J, Montgomery RR, Zimmerman Program Investigators) Res Pract Thromb Haemost 2023 Oct;7(7):102232 PMID: 38077814 PMCID: PMC10704516 SCOPUS ID: 2-s2.0-85175701842 12/11/2023       2 Citations
  • The common VWF variant p.Y1584C: detailed pathogenic examination of an enigmatic sequence change. (Christopherson PA, Tijet N, Haberichter SL, Flood VH, Ross J, Notley C, Rawley O, Montgomery RR, Zimmerman Project Investigators, James PD, Lillicrap D) J Thromb Haemost 2024 Mar;22(3):666-675 PMID: 38040335 PMCID: PMC10922911 SCOPUS ID: 2-s2.0-85181082101 12/02/2023       10 Citations
  • Von Willebrand Factor (VWF) multiplex activity assay differentiation of type 1 von Willebrand Disease (VWD) and variant VWD. (Roberts JC, Christopherson PA, Tarantino MD, Gonzales SE, Morateck PA, Perry CL, Flood VH, Abshire TC, Montgomery RR, Zimmerman Program Investigators) Haemophilia 2024 Jan;30(1):161-168 PMID: 38013388 PMCID: PMC10842138 SCOPUS ID: 2-s2.0-85177751625 11/28/2023       1 Citation
  • Characterization of copy-number variants in a large cohort of patients with von Willebrand disease reveals a relationship between disrupted regions and disease type (Sadler B, Christopherson PA, Perry CL, Bellissimo DB, Haberichter SL, Haller G, Antunes L, Flood VH, Di Paola J, Montgomery RR) Research and Practice in Thrombosis and Haemostasis October 2023;7(7) SCOPUS ID: 2-s2.0-85175701842 10/01/2023       2 Citations
  • Building the foundation for a community-generated national research blueprint for inherited bleeding disorders: research priorities for mucocutaneous bleeding disorders. (Sidonio RF Jr, Bryant PC, Di Paola J, Hale S, Heiman M, Horowitz GS, Humphrey C, Jaffray J, Joyner LC, Kasthuri R, Konkle BA, Kouides PA, Montgomery R, Neeves K, Randi AM, Scappe N, Tarango C, Tickle K, Trapane P, Wang M, Waters B, Flood VH) Expert Rev Hematol 2023 Mar;16(sup1):39-54 PMID: 36920856 SCOPUS ID: 2-s2.0-85150353015 03/16/2023       15 Citations
  • Variability in International Society on Thrombosis and Haemostasis-Scientific and Standardization Committee endorsed Bleeding Assessment Tool (ISTH-BAT) score with normal aging in healthy females: contributory factors and clinical significance. (Doherty D, Grabell J, Christopherson PA, Montgomery RR, Coller BS, Lavin M, O'Donnell JS, James PD, Zimmerman Program Investigators) J Thromb Haemost 2023 Apr;21(4):880-886 PMID: 36696194 PMCID: PMC11008594 SCOPUS ID: 2-s2.0-85150980164 01/26/2023       31 Citations
  • Ristocetin dependent cofactor activity in von Willebrand disease diagnosis: Limitations of relying on a single measure. (Christopherson PA, Haberichter SL, Flood VH, Sicking UO, Abshire TC, Montgomery RR, Zimmerman Program Investigators) Res Pract Thromb Haemost 2022 Oct;6(7):e12807 PMID: 36381287 PMCID: PMC9637542 SCOPUS ID: 2-s2.0-85142096764 11/17/2022       9 Citations
  • Longitudinal bleeding assessment in von Willebrand disease utilizing an interim bleeding score. (Lavin M, Christopherson P, Grabell J, Abshire T, Flood V, Haberichter SL, Lillicrap D, O'Donnell JS, Montgomery RR, James PD) J Thromb Haemost 2022 Oct;20(10):2246-2254 PMID: 35780487 PMCID: PMC10193460 SCOPUS ID: 2-s2.0-85134729733 07/04/2022       7 Citations
  • Molecular pathogenesis and heterogeneity in type 3 VWD families in U.S. Zimmerman program. (Christopherson PA, Haberichter SL, Flood VH, Perry CL, Sadler BE, Bellissimo DB, Di Paola J, Montgomery RR, Zimmerman Program Investigators) J Thromb Haemost 2022 Jul;20(7):1576-1588 PMID: 35343054 PMCID: PMC11892521 SCOPUS ID: 2-s2.0-85133103088 03/29/2022       18 Citations
  • Laboratory assays of VWF activity and use of desmopressin trials in the diagnosis of VWD: a systematic review and meta-analysis. (Kalot MA, Husainat N, Abughanimeh O, Diab O, El Alayli A, Tayiem S, Madoukh B, Dimassi A, Qureini A, Ameer B, Eikenboom J, Giraud N, Haberichter S, Jacobs-Pratt V, Konkle BA, McRae S, Montgomery R, O'Donnell JS, Brignardello-Petersen R, Flood V, Connell NT, James P, Mustafa RA) Blood Adv 2022 Jun 28;6(12):3735-3745 PMID: 35192687 PMCID: PMC9631556 SCOPUS ID: 2-s2.0-85133138416 02/23/2022       10 Citations
  • The impact of aberrant von Willebrand factor-GPIbα interaction on megakaryopoiesis and platelets in humanized type 2B von Willebrand disease model mouse. (Kanaji S, Morodomi Y, Weiler H, Zarpellon A, Montgomery RR, Ruggeri ZM, Kanaji T) Haematologica 2022 Sep 01;107(9):2133-2143 PMID: 35142156 PMCID: PMC9425322 SCOPUS ID: 2-s2.0-85131561060 02/11/2022       4 Citations
  • A novel mouse model of type 2N VWD was developed by CRISPR/Cas9 gene editing and recapitulates human type 2N VWD. (Shi Q, Fahs SA, Mattson JG, Yu H, Perry CL, Morateck PA, Schroeder JA, Rapten J, Weiler H, Montgomery RR) Blood Adv 2022 May 10;6(9):2778-2790 PMID: 35015821 PMCID: PMC9092403 SCOPUS ID: 2-s2.0-85130105632 01/12/2022       7 Citations
  • von Willebrand factor levels in the diagnosis of von Willebrand disease: a systematic review and meta-analysis. (Kalot MA, Husainat N, El Alayli A, Abughanimeh O, Diab O, Tayiem S, Madoukh B, Dimassi AB, Qureini A, Ameer B, Eikenboom JCJ, Giraud N, McLintock C, McRae S, Montgomery RR, O'Donnell JS, Scappe N, Sidonio RF, Brignardello-Petersen R, Flood VH, Connell NT, James PD, Mustafa RA) Blood Adv 2022 Jan 11;6(1):62-71 PMID: 34610118 PMCID: PMC8753202 SCOPUS ID: 2-s2.0-85123083589 10/06/2021       30 Citations
  • Screening for von Willebrand disease does not impact posttonsillectomy bleeding in a low-risk population. (Digiandomenico S, Conley SF, Johnson VP, Christopherson PA, Haberichter SL, Zhang J, Simpson P, Abshire TC, Montgomery RR, Flood VH) Pediatr Blood Cancer 2021 Dec;68(12):e29371 PMID: 34606172 PMCID: PMC8919995 SCOPUS ID: 2-s2.0-85116391259 10/05/2021    
  • Bleeding assessment tools in the diagnosis of VWD in adults and children: a systematic review and meta-analysis of test accuracy. (Kalot MA, Husainat N, Tayiem S, El Alayli A, Dimassi AB, Diab O, Abughanimeh O, Madoukh B, Qureini A, Ameer B, Di Paola J, Eikenboom JCJ, Jacobs-Pratt V, McLintock C, Montgomery R, O'Donnell JS, Sidonio R, Brignardello-Petersen R, Flood V, Connell NT, James PD, Mustafa RA) Blood Adv 2021 Dec 14;5(23):5023-5031 PMID: 34597385 PMCID: PMC9153010 SCOPUS ID: 2-s2.0-85121759469 10/02/2021       12 Citations
  • Thromboelastometry assessment of hemostatic properties in various murine models with coagulopathy and the effect of factor VIII therapeutics. (Schroeder JA, Kuether EA, Fang J, Jing W, Weiler H, Wilcox DA, Montgomery RR, Shi Q) J Thromb Haemost 2021 Oct;19(10):2417-2427 PMID: 34245090 PMCID: PMC8865566 SCOPUS ID: 2-s2.0-85111140299 07/11/2021       7 Citations
  • ASH ISTH NHF WFH 2021 guidelines on the diagnosis of von Willebrand disease. (James PD, Connell NT, Ameer B, Di Paola J, Eikenboom J, Giraud N, Haberichter S, Jacobs-Pratt V, Konkle B, McLintock C, McRae S, R Montgomery R, O'Donnell JS, Scappe N, Sidonio R, Flood VH, Husainat N, Kalot MA, Mustafa RA) Blood Adv 2021 Jan 12;5(1):280-300 PMID: 33570651 PMCID: PMC7805340 SCOPUS ID: 2-s2.0-85099835799 02/12/2021       436 Citations
  • von Willebrand factor antigen levels are associated with burden of rare nonsynonymous variants in the VWF gene. (Sadler B, Christopherson PA, Haller G, Montgomery RR, Di Paola J) Blood 2021 Jun 10;137(23):3277-3283 PMID: 33556167 PMCID: PMC8351900 SCOPUS ID: 2-s2.0-85107840652 02/09/2021       21 Citations
  • von Willebrand disease: proposing definitions for future research. (Connell NT, James PD, Brignardello-Petersen R, Abdul-Kadir R, Ameer B, Arapshian A, Couper S, Di Paola J, Eikenboom J, Giraud N, Grow JM, Haberichter S, Jacobs-Pratt V, Konkle BA, Kouides P, Laffan M, Lavin M, Leebeek FWG, McLintock C, McRae S, Montgomery R, O'Brien SH, O'Donnell JS, Ozelo MC, Scappe N, Sidonio R, Tosetto A, Weyand AC, Kalot MA, Husainat N, Mustafa RA, Flood VH) Blood Adv 2021 Jan 26;5(2):565-569 PMID: 33496750 PMCID: PMC7839375 SCOPUS ID: 2-s2.0-85099826171 01/27/2021       37 Citations
  • Laboratory variability in the diagnosis of type 2 VWD variants. (DiGiandomenico S, Christopherson PA, Haberichter SL, Abshire TC, Montgomery RR, Flood VH, Zimmerman Program Investigators) J Thromb Haemost 2021 Jan;19(1):131-138 PMID: 33049112 PMCID: PMC7790985 SCOPUS ID: 2-s2.0-85100279861 10/14/2020       18 Citations
  • von Willebrand factor variant D1472H has no effect in mice with humanized VWF-platelet interactions. (Lohmeier HK, Slobodianuk TL, Kanaji S, Haberichter SL, Montgomery RR, Flood VH) Blood Adv 2020 Sep 08;4(17):4065-4068 PMID: 32870970 PMCID: PMC7479953 SCOPUS ID: 2-s2.0-85100184214 09/02/2020       3 Citations
  • Comparison of von Willebrand factor platelet-binding activity assays: ELISA overreads type 2B with loss of HMW multimers. (Szederjesi A, Baronciani L, Budde U, Castaman G, Colpani P, Lawrie AS, Liu Y, Montgomery R, Peyvandi F, Schneppenheim R, Patzke J, Bodó I) J Thromb Haemost 2020 Oct;18(10):2513-2523 PMID: 32573891 PMCID: PMC7722054 SCOPUS ID: 2-s2.0-85089858578 06/24/2020       8 Citations
  • A rat model of severe VWD by elimination of the VWF gene using CRISPR/Cas9. (Garcia J, Flood VH, Haberichter SL, Fahs SA, Mattson JG, Geurts AM, Zogg M, Weiler H, Shi Q, Montgomery RR) Res Pract Thromb Haemost 2020 Jan;4(1):64-71 PMID: 31989086 PMCID: PMC6971331 SCOPUS ID: 2-s2.0-85105291983 01/29/2020       5 Citations
  • von Willebrand factor binding to myosin assists in coagulation. (Flood VH, Slobodianuk TL, Keesler D, Lohmeier HK, Fahs S, Zhang L, Simpson P, Montgomery RR) Blood Adv 2020 Jan 14;4(1):174-180 PMID: 31935285 PMCID: PMC6960459 SCOPUS ID: 2-s2.0-85078090866 01/15/2020       7 Citations
  • Low VWF levels in children and lack of association with bleeding in children undergoing tonsillectomy. (Gill JC, Conley SF, Johnson VP, Christopherson PA, Haberichter SL, Diaz CD, Strong TC, Zhang J, Simpson P, Abshire TC, Montgomery RR, Flood VH) Blood Adv 2020 Jan 14;4(1):100-105 PMID: 31905240 PMCID: PMC6960478 SCOPUS ID: 2-s2.0-85078147321 01/07/2020       29 Citations
  • The severe spontaneous bleeding phenotype in a novel hemophilia A rat model is rescued by platelet FVIII expression. (Shi Q, Mattson JG, Fahs SA, Geurts AM, Weiler H, Montgomery RR) Blood Adv 2020 Jan 14;4(1):55-65 PMID: 31899798 PMCID: PMC6960468 SCOPUS ID: 2-s2.0-85078174834 01/04/2020       12 Citations
  • An international survey to inform priorities for new guidelines on von Willebrand disease. (Kalot MA, Al-Khatib M, Connell NT, Flood V, Brignardello-Petersen R, James P, Mustafa RA, VWD working group) Haemophilia 2020 Jan;26(1):106-116 PMID: 31769905 PMCID: PMC7041556 SCOPUS ID: 2-s2.0-85076016135 11/27/2019       38 Citations
  • How we approach: Training pediatric coagulationists. (Thornburg CD, Montgomery RR, Pipe SW) Pediatr Blood Cancer 2019 Dec;66(12):e27982 PMID: 31486588 SCOPUS ID: 2-s2.0-85071949174 09/06/2019       1 Citation
  • The impact of GPIbα on platelet-targeted FVIII gene therapy in hemophilia A mice with pre-existing anti-FVIII immunity. (Chen J, Schroeder JA, Luo X, Montgomery RR, Shi Q) J Thromb Haemost 2019 Mar;17(3):449-459 PMID: 30609275 PMCID: PMC6397061 SCOPUS ID: 2-s2.0-85061041842 01/05/2019       18 Citations
  • Humanized GPIbα-von Willebrand factor interaction in the mouse. (Kanaji S, Orje JN, Kanaji T, Kamikubo Y, Morodomi Y, Chen Y, Zarpellon A, Eberhardt J, Forli S, Fahs SA, Sood R, Haberichter SL, Montgomery RR, Ruggeri ZM) Blood Adv 2018 Oct 09;2(19):2522-2532 PMID: 30287479 PMCID: PMC6177644 SCOPUS ID: 2-s2.0-85069786057 10/06/2018       16 Citations
  • Von Willebrand disease in the United States: perspective from the Zimmerman program. (Flood VH, Abshire TC, Christopherson PA, Friedman KD, Cox Gill J, Montgomery RR, Haberichter SL, Zimmerman Program Investigators) Ann Blood 2018 Jan;3 PMID: 30135959 PMCID: PMC6100783 08/24/2018    
  • The endothelial cell receptor stabilin-2 regulates VWF-FVIII complex half-life and immunogenicity. (Swystun LL, Lai JD, Notley C, Georgescu I, Paine AS, Mewburn J, Nesbitt K, Schledzewski K, Géraud C, Kzhyshkowska J, Goerdt S, Hopman W, Montgomery RR, James PD, Lillicrap D) J Clin Invest 2018 Aug 31;128(9):4057-4073 PMID: 30124466 PMCID: PMC6118640 SCOPUS ID: 2-s2.0-85052566583 08/21/2018       76 Citations
  • An international collaborative study to compare different von Willebrand factor glycoprotein Ib binding activity assays: the COMPASS-VWF study (Szederjesi A, Baronciani L, Budde U, Castaman G, Lawrie AS, Liu Y, Montgomery R, Peyvandi F, Schneppenheim R, Várkonyi A, Patzke J, Bodó I) Journal of Thrombosis and Haemostasis August 2018;16(8):1604-1613 SCOPUS ID: 2-s2.0-85050625264 08/01/2018       15 Citations
  • Common VWF sequence variants associated with higher VWF and FVIII are less frequent in subjects diagnosed with type 1 VWD. (Flood VH, Johnsen JM, Kochelek C, Slobodianuk TL, Christopherson PA, Haberichter SL, Udani R, Bellissimo DB, Friedman KD, Montgomery RR) Res Pract Thromb Haemost 2018 Apr;2(2):390-398 PMID: 30046743 PMCID: PMC5974909 SCOPUS ID: 2-s2.0-85076700342 07/27/2018       8 Citations
  • Clinical and laboratory phenotype variability in type 2M von Willebrand disease. (Doruelo AL, Haberichter SL, Christopherson PA, Boggio LN, Gupta S, Lentz SR, Shapiro AD, Montgomery RR, Flood VH) J Thromb Haemost 2017 Aug;15(8):1559-1566 PMID: 28544236 PMCID: PMC5538962 SCOPUS ID: 2-s2.0-85021241191 05/26/2017       21 Citations
  • Gene therapy (Shi Q, Montgomery RR) Platelets in Thrombotic and Non Thrombotic Disorders Pathophysiology Pharmacology and Therapeutics an Update 8 March 2017:1431-1445 SCOPUS ID: 2-s2.0-85055916604 03/08/2017    
  • Gene therapy Platelets in Thrombotic and Non-Thrombotic Disorders: Pathophysiology, Pharmacology and Therapeutics: an Update 8 March 2017:1431-1445 03/08/2017    
  • What have we learned from large population studies of von Willebrand disease? (Montgomery RR, Flood VH) Hematology Am Soc Hematol Educ Program 2016 Dec 02;2016(1):670-677 PMID: 27913545 PMCID: PMC5518316 SCOPUS ID: 2-s2.0-85020267077 12/04/2016       12 Citations
  • Life in the shadow of a dominant partner: the FVIII-VWF association and its clinical implications for hemophilia A. (Pipe SW, Montgomery RR, Pratt KP, Lenting PJ, Lillicrap D) Blood 2016 Oct 20;128(16):2007-2016 PMID: 27587878 PMCID: PMC5073181 SCOPUS ID: 2-s2.0-84992390506 09/03/2016       203 Citations
  • Targeting factor VIII expression to platelets for hemophilia A gene therapy does not induce an apparent thrombotic risk in mice. (Baumgartner CK, Mattson JG, Weiler H, Shi Q, Montgomery RR) J Thromb Haemost 2017 Jan;15(1):98-109 PMID: 27496751 PMCID: PMC5280575 SCOPUS ID: 2-s2.0-84997796223 08/09/2016       22 Citations
  • Identification and characterization of the elusive mutation causing the historical von Willebrand Disease type IIC Miami. (Obser T, Ledford-Kraemer M, Oyen F, Brehm MA, Denis CV, Marschalek R, Montgomery RR, Sadler JE, Schneppenheim S, Budde U, Schneppenheim R) J Thromb Haemost 2016 Sep;14(9):1725-35 PMID: 27344059 PMCID: PMC5035592 SCOPUS ID: 2-s2.0-84988462405 06/28/2016       12 Citations
  • The heads and the tails of malaria and VWF. (Montgomery RR) Blood 2016 Mar 03;127(9):1081-2 PMID: 26941390 SCOPUS ID: 2-s2.0-84960412121 03/05/2016       3 Citations
  • Rapid discrimination of the phenotypic variants of von Willebrand disease. (Roberts JC, Morateck PA, Christopherson PA, Yan K, Hoffmann RG, Gill JC, Montgomery RR, Zimmerman Program Investigators) Blood 2016 May 19;127(20):2472-80 PMID: 26917779 PMCID: PMC4874227 SCOPUS ID: 2-s2.0-84974623429 02/27/2016       21 Citations
  • Clinical and laboratory variability in a cohort of patients diagnosed with type 1 VWD in the United States. (Flood VH, Christopherson PA, Gill JC, Friedman KD, Haberichter SL, Bellissimo DB, Udani RA, Dasgupta M, Hoffmann RG, Ragni MV, Shapiro AD, Lusher JM, Lentz SR, Abshire TC, Leissinger C, Hoots WK, Manco-Johnson MJ, Gruppo RA, Boggio LN, Montgomery KT, Goodeve AC, James PD, Lillicrap D, Peake IR, Montgomery RR) Blood 2016 May 19;127(20):2481-8 PMID: 26862110 PMCID: PMC4874228 SCOPUS ID: 2-s2.0-84974556876 02/11/2016       119 Citations
  • The immunogenicity of platelet-derived FVIII in hemophilia A mice with or without preexisting anti-FVIII immunity. (Chen Y, Schroeder JA, Chen J, Luo X, Baumgartner CK, Montgomery RR, Hu J, Shi Q) Blood 2016 Mar 10;127(10):1346-54 PMID: 26668132 PMCID: PMC4786841 SCOPUS ID: 2-s2.0-84960904100 12/17/2015       24 Citations
  • Comparison of platelet-derived and plasma factor VIII efficacy using a novel native whole blood thrombin generation assay. (Baumgartner CK, Zhang G, Kuether EL, Weiler H, Shi Q, Montgomery RR) J Thromb Haemost 2015 Dec;13(12):2210-9 PMID: 26453193 PMCID: PMC4715732 SCOPUS ID: 2-s2.0-84958773657 10/11/2015       15 Citations
  • Corrigendum to "Characterization of Zebrafish von Willebrand Factor Reveals Conservation of Domain Structure, Multimerization, and Intracellular Storage". (Ghosh A, Vo A, Twiss BK, Kretz CA, Jozwiak MA, Montgomery RR, Shavit JA) Adv Hematol 2015;2015:526854 PMID: 26357516 PMCID: PMC4556866 SCOPUS ID: 2-s2.0-84940732112 09/12/2015    
  • Variable content of von Willebrand factor mutant monomer drives the phenotypic variability in a family with von Willebrand disease. (Chen J, Hinckley JD, Haberichter S, Jacobi P, Montgomery R, Flood VH, Wong R, Interlandi G, Chung DW, López JA, Di Paola J) Blood 2015 Jul 09;126(2):262-9 PMID: 26019279 PMCID: PMC4497966 SCOPUS ID: 2-s2.0-84937953557 05/29/2015       18 Citations
  • The important role of von Willebrand factor in platelet-derived FVIII gene therapy for murine hemophilia A in the presence of inhibitory antibodies. (Shi Q, Schroeder JA, Kuether EL, Montgomery RR) J Thromb Haemost 2015 Jul;13(7):1301-9 PMID: 25955153 PMCID: PMC4496307 SCOPUS ID: 2-s2.0-84935446637 05/09/2015       21 Citations
  • Platelet-dependent von Willebrand factor activity. Nomenclature and methodology: communication from the SSC of the ISTH. (Bodó I, Eikenboom J, Montgomery R, Patzke J, Schneppenheim R, Di Paola J, von Willebrand factor Subcommittee of the Standardization and Scientific Committee of the International Society for Thrombosis and Haemostasis) J Thromb Haemost 2015 Jul;13(7):1345-50 PMID: 25858564 PMCID: PMC5576173 SCOPUS ID: 2-s2.0-84935687838 04/11/2015       142 Citations
  • Crucial role for the VWF A1 domain in binding to type IV collagen. (Flood VH, Schlauderaff AC, Haberichter SL, Slobodianuk TL, Jacobi PM, Bellissimo DB, Christopherson PA, Friedman KD, Gill JC, Hoffmann RG, Montgomery RR, Zimmerman Program Investigators) Blood 2015 Apr 02;125(14):2297-304 PMID: 25662333 PMCID: PMC4383803 SCOPUS ID: 2-s2.0-84926664083 02/11/2015       90 Citations
  • Normal range of bleeding scores for the ISTH-BAT: adult and pediatric data from the merging project. (Elbatarny M, Mollah S, Grabell J, Bae S, Deforest M, Tuttle A, Hopman W, Clark DS, Mauer AC, Bowman M, Riddel J, Christopherson PA, Montgomery RR, Zimmerman Program Investigators, Rand ML, Coller B, James PD) Haemophilia 2014 Nov;20(6):831-5 PMID: 25196510 PMCID: PMC4251588 SCOPUS ID: 2-s2.0-84942517095 09/10/2014       287 Citations
  • Non-myeloablative conditioning with busulfan before hematopoietic stem cell transplantation leads to phenotypic correction of murine Bernard-Soulier syndrome. (Kanaji S, Fahs SA, Ware J, Montgomery RR, Shi Q) J Thromb Haemost 2014 Oct;12(10):1726-32 PMID: 25066812 PMCID: PMC4194147 SCOPUS ID: 2-s2.0-84907878326 07/30/2014       6 Citations
  • A conditional knockout mouse model reveals endothelial cells as the principal and possibly exclusive source of plasma factor VIII. (Fahs SA, Hille MT, Shi Q, Weiler H, Montgomery RR) Blood 2014 Jun 12;123(24):3706-13 PMID: 24705491 PMCID: PMC4055921 SCOPUS ID: 2-s2.0-84902594994 04/08/2014       159 Citations
  • Evaluation of von Willebrand factor and von Willebrand factor propeptide in models of vascular endothelial cell activation, perturbation, and/or injury. (Brott DA, Katein A, Thomas H, Lawton M, Montgomery RR, Richardson RJ, Louden CS) Toxicol Pathol 2014 Jun;42(4):672-83 PMID: 24499802 PMCID: PMC4222990 SCOPUS ID: 2-s2.0-84902078130 02/07/2014       18 Citations
  • Platelet gene therapy corrects the hemophilic phenotype in immunocompromised hemophilia A mice transplanted with genetically manipulated human cord blood stem cells. (Shi Q, Kuether EL, Chen Y, Schroeder JA, Fahs SA, Montgomery RR) Blood 2014 Jan 16;123(3):395-403 PMID: 24269957 PMCID: PMC3894495 SCOPUS ID: 2-s2.0-84897018747 11/26/2013       45 Citations
  • Platelet hyperreactivity explains the bleeding abnormality and macrothrombocytopenia in a murine model of sitosterolemia. (Kanaji T, Kanaji S, Montgomery RR, Patel SB, Newman PJ) Blood 2013 Oct 10;122(15):2732-42 PMID: 23926302 PMCID: PMC3795464 SCOPUS ID: 2-s2.0-84888251628 08/09/2013       61 Citations
  • Markers of vascular perturbation correlate with airway structural change in asthma. (Johansson MW, Kruger SJ, Schiebler ML, Evans MD, Sorkness RL, Denlinger LC, Busse WW, Jarjour NN, Montgomery RR, Mosher DF, Fain SB) Am J Respir Crit Care Med 2013 Jul 15;188(2):167-78 PMID: 23855693 PMCID: PMC3778758 SCOPUS ID: 2-s2.0-84881157401 07/17/2013       21 Citations
  • The C-type lectin receptor CLEC4M binds, internalizes, and clears von Willebrand factor and contributes to the variation in plasma von Willebrand factor levels. (Rydz N, Swystun LL, Notley C, Paterson AD, Riches JJ, Sponagle K, Boonyawat B, Montgomery RR, James PD, Lillicrap D) Blood 2013 Jun 27;121(26):5228-37 PMID: 23529928 PMCID: PMC3722568 SCOPUS ID: 2-s2.0-84884180924 03/27/2013       114 Citations
  • No increase in bleeding identified in type 1 VWD subjects with D1472H sequence variation. (Flood VH, Friedman KD, Gill JC, Haberichter SL, Christopherson PA, Branchford BR, Hoffmann RG, Abshire TC, Dunn AL, Di Paola JA, Hoots WK, Brown DL, Leissinger C, Lusher JM, Ragni MV, Shapiro AD, Montgomery RR) Blood 2013 May 02;121(18):3742-4 PMID: 23520336 PMCID: PMC3643771 SCOPUS ID: 2-s2.0-84879719268 03/23/2013       34 Citations
  • Third Åland islands conference on von Willebrand disease, 26-28 September 2012: meeting report. (Berntorp E, Fuchs B, Makris M, Montgomery R, Flood V, O'Donnell JS, Federici AB, Lillicrap D, James P, Budde U, Morfini M, Petrini P, Austin S, Kannicht C, Jiménez-Yuste V, Lee C) Haemophilia 2013 Mar;19 Suppl 3(0 3):1-18 PMID: 23383607 PMCID: PMC4164969 SCOPUS ID: 2-s2.0-84873425397 02/13/2013       5 Citations
  • Collagen binding provides a sensitive screen for variant von Willebrand disease. (Flood VH, Gill JC, Friedman KD, Christopherson PA, Jacobi PM, Hoffmann RG, Montgomery RR, Haberichter SL, Zimmerman Program Investigators) Clin Chem 2013 Apr;59(4):684-91 PMID: 23340442 PMCID: PMC3852672 SCOPUS ID: 2-s2.0-84875860574 01/24/2013       63 Citations
  • Characterization of zebrafish von Willebrand factor reveals conservation of domain structure, multimerization, and intracellular storage. (Ghosh A, Vo A, Twiss BK, Kretz CA, Jozwiak MA, Montgomery RR, Shavit JA) Adv Hematol 2012;2012:214209 PMID: 23049555 PMCID: PMC3462383 SCOPUS ID: 2-s2.0-84867344585 10/11/2012       19 Citations
  • von Willebrand's disease: a report from a meeting in the Åland islands. (Berntorp E, Peake I, Budde U, Laffan M, Montgomery R, Windyga J, Goodeve A, Petrini P, von Depka M, Miesbach W, Lillicrap D, Federici AB, Lassila R, White G) Haemophilia 2012 Sep;18 Suppl 6(0 6):1-13 PMID: 22906074 PMCID: PMC4170876 SCOPUS ID: 2-s2.0-84865387027 08/29/2012       14 Citations
  • Factor VIII inhibitors: von Willebrand factor makes a difference in vitro and in vivo. (Shi Q, Kuether EL, Schroeder JA, Perry CL, Fahs SA, Cox Gill J, Montgomery RR) J Thromb Haemost 2012 Nov;10(11):2328-37 PMID: 22908929 PMCID: PMC3670966 SCOPUS ID: 2-s2.0-84868144084 08/23/2012       25 Citations
  • Standardization of von Willebrand factor propeptide: value assignment to the WHO 6th IS Factor VIII/von Willebrand factor, plasma (07/316). (Hubbard AR, Hamill M, Eikenboom HC, Montgomery RR, Mertens K, Haberichter S, SSC sub-committee on von Willebrand factor of ISTH) J Thromb Haemost 2012 May;10(5):959-60 PMID: 22696769 PMCID: PMC4196679 SCOPUS ID: 2-s2.0-84860455038 06/15/2012       8 Citations
  • Contribution of platelet vs. endothelial VWF to platelet adhesion and hemostasis. (Kanaji S, Fahs SA, Shi Q, Haberichter SL, Montgomery RR) J Thromb Haemost 2012 Aug;10(8):1646-52 PMID: 22642380 PMCID: PMC3419786 SCOPUS ID: 2-s2.0-84865237107 05/31/2012       118 Citations
  • Lentivirus-mediated platelet gene therapy of murine hemophilia A with pre-existing anti-factor VIII immunity. (Kuether EL, Schroeder JA, Fahs SA, Cooley BC, Chen Y, Montgomery RR, Wilcox DA, Shi Q) J Thromb Haemost 2012 Aug;10(8):1570-80 PMID: 22632092 PMCID: PMC3419807 SCOPUS ID: 2-s2.0-84864333652 05/29/2012       94 Citations
  • Comparison of type I, type III and type VI collagen binding assays in diagnosis of von Willebrand disease. (Flood VH, Gill JC, Christopherson PA, Wren JS, Friedman KD, Haberichter SL, Hoffmann RG, Montgomery RR) J Thromb Haemost 2012 Jul;10(7):1425-32 PMID: 22507643 PMCID: PMC3809762 SCOPUS ID: 2-s2.0-84863455676 04/18/2012       52 Citations
  • Critical von Willebrand factor A1 domain residues influence type VI collagen binding. (Flood VH, Gill JC, Christopherson PA, Bellissimo DB, Friedman KD, Haberichter SL, Lentz SR, Montgomery RR) J Thromb Haemost 2012 Jul;10(7):1417-24 PMID: 22507569 PMCID: PMC3809952 SCOPUS ID: 2-s2.0-84863422773 04/18/2012       67 Citations
  • von Willebrand factor (VWF) propeptide binding to VWF D'D3 domain attenuates platelet activation and adhesion. (Madabhushi SR, Shang C, Dayananda KM, Rittenhouse-Olson K, Murphy M, Ryan TE, Montgomery RR, Neelamegham S) Blood 2012 May 17;119(20):4769-78 PMID: 22452980 PMCID: PMC3367877 SCOPUS ID: 2-s2.0-84861208099 03/29/2012       28 Citations
  • Platelet and endothelial expression of clotting factors for the treatment of hemophilia. (Montgomery RR, Shi Q) Thromb Res 2012 May;129 Suppl 2(Suppl 2):S46-8 PMID: 22421106 PMCID: PMC3581347 SCOPUS ID: 2-s2.0-84859802515 03/17/2012       16 Citations
  • Intravascular recovery of VWF and FVIII following intraperitoneal injection and differences from intravenous and subcutaneous injection in mice. (Shi Q, Kuether EL, Schroeder JA, Fahs SA, Montgomery RR) Haemophilia 2012 Jul;18(4):639-46 PMID: 22221819 PMCID: PMC3323668 SCOPUS ID: 2-s2.0-84863193826 01/10/2012       22 Citations
  • VWF mutations and new sequence variations identified in healthy controls are more frequent in the African-American population. (Bellissimo DB, Christopherson PA, Flood VH, Gill JC, Friedman KD, Haberichter SL, Shapiro AD, Abshire TC, Leissinger C, Hoots WK, Lusher JM, Ragni MV, Montgomery RR) Blood 2012 Mar 01;119(9):2135-40 PMID: 22197721 PMCID: PMC3311248 SCOPUS ID: 2-s2.0-84857720362 12/27/2011       90 Citations
  • Von Willebrand disease in the United States: a perspective from Wisconsin. (Flood VH, Gill JC, Friedman KD, Bellissimo DB, Haberichter SL, Montgomery RR) Semin Thromb Hemost 2011 Jul;37(5):528-34 PMID: 22102196 PMCID: PMC3807766 SCOPUS ID: 2-s2.0-81755171917 11/22/2011       27 Citations
  • Correction of murine Bernard-Soulier syndrome by lentivirus-mediated gene therapy. (Kanaji S, Kuether EL, Fahs SA, Schroeder JA, Ware J, Montgomery RR, Shi Q) Mol Ther 2012 Mar;20(3):625-32 PMID: 22044935 PMCID: PMC3293608 SCOPUS ID: 2-s2.0-84857781525 11/03/2011       30 Citations
  • Von Willebrand Factor Structure and Function (Montgomery RR, Haberichter SL) Von Willebrand Disease Basic and Clinical Aspects 21 March 2011:30-48 SCOPUS ID: 2-s2.0-84885515502 03/21/2011       4 Citations
  • Preface (Federici AB, Lee CA, Berntorp EE, Lillicrap D, Montgomery RR) Von Willebrand Disease Basic and Clinical Aspects 21 March 2011 SCOPUS ID: 2-s2.0-84885486217 03/21/2011    
  • Von Willebrand Disease: Basic and Clinical Aspects (Federici AB, Lee CA, Berntorp EE, Lillicrap D, Montgomery RR) Von Willebrand Disease Basic and Clinical Aspects 21 March 2011 SCOPUS ID: 2-s2.0-84877039098 03/21/2011       5 Citations
  • Alternative strategies for gene therapy of hemophilia. (Montgomery RR, Shi Q) Hematology Am Soc Hematol Educ Program 2010;2010:197-202 PMID: 21239794 PMCID: PMC3383974 SCOPUS ID: 2-s2.0-79955004711 01/18/2011       5 Citations
  • Gain-of-function GPIb ELISA assay for VWF activity in the Zimmerman Program for the Molecular and Clinical Biology of VWD. (Flood VH, Gill JC, Morateck PA, Christopherson PA, Friedman KD, Haberichter SL, Hoffmann RG, Montgomery RR) Blood 2011 Feb 10;117(6):e67-74 PMID: 21148813 PMCID: PMC3056647 SCOPUS ID: 2-s2.0-79951469339 12/15/2010       105 Citations
  • von Willebrand Disease: Biologic Diagnosis (Flood VH, Montgomery RR) Textbook of Hemophilia Second Edition 13 August 2010:294-301 SCOPUS ID: 2-s2.0-84885794685 08/13/2010       1 Citation
  • von Willebrand's disease diagnosis and laboratory issues. (Castaman G, Montgomery RR, Meschengieser SS, Haberichter SL, Woods AI, Lazzari MA) Haemophilia 2010 Jul;16 Suppl 5(0 5):67-73 PMID: 20590859 PMCID: PMC4313748 SCOPUS ID: 2-s2.0-77955045227 07/16/2010       26 Citations
  • Unique strategies for therapeutic gene transfer in haemophilia A and haemophilia BWFH State-of-the-Art Session on Therapeutic Gene Transfer Buenos Aires, Argentina. (Montgomery RR, Monahan PE, Ozelo MC) Haemophilia 2010 Jul;16 Suppl 5(Suppl 5):29-34 PMID: 20590853 PMCID: PMC5592798 SCOPUS ID: 2-s2.0-77955030405 07/16/2010       6 Citations
  • Platelets as delivery systems for disease treatments. (Shi Q, Montgomery RR) Adv Drug Deliv Rev 2010 Sep 30;62(12):1196-203 PMID: 20619307 PMCID: PMC2991519 SCOPUS ID: 2-s2.0-78649321428 07/14/2010       55 Citations
  • Targeting FVIII expression to endothelial cells regenerates a releasable pool of FVIII and restores hemostasis in a mouse model of hemophilia A. (Shi Q, Fahs SA, Kuether EL, Cooley BC, Weiler H, Montgomery RR) Blood 2010 Oct 21;116(16):3049-57 PMID: 20606161 PMCID: PMC2974610 SCOPUS ID: 2-s2.0-77958193310 07/08/2010       45 Citations
  • Factor IX ectopically expressed in platelets can be stored in alpha-granules and corrects the phenotype of hemophilia B mice. (Zhang G, Shi Q, Fahs SA, Kuether EL, Walsh CE, Montgomery RR) Blood 2010 Aug 26;116(8):1235-43 PMID: 20445020 PMCID: PMC2938234 SCOPUS ID: 2-s2.0-77955921912 05/07/2010       49 Citations
  • Absent collagen binding in a VWF A3 domain mutant: utility of the VWF:CB in diagnosis of VWD. (Flood VH, Lederman CA, Wren JS, Christopherson PA, Friedman KD, Hoffmann RG, Montgomery RR) J Thromb Haemost 2010 Jun;8(6):1431-3 PMID: 20345715 PMCID: PMC3892206 SCOPUS ID: 2-s2.0-77954496769 03/30/2010       83 Citations
  • Common VWF exon 28 polymorphisms in African Americans affecting the VWF activity assay by ristocetin cofactor. (Flood VH, Gill JC, Morateck PA, Christopherson PA, Friedman KD, Haberichter SL, Branchford BR, Hoffmann RG, Abshire TC, Di Paola JA, Hoots WK, Leissinger C, Lusher JM, Ragni MV, Shapiro AD, Montgomery RR) Blood 2010 Jul 15;116(2):280-6 PMID: 20231421 PMCID: PMC2910611 SCOPUS ID: 2-s2.0-77955499972 03/17/2010       170 Citations
  • Limitations of the ristocetin cofactor assay in measurement of von Willebrand factor function. (Flood VH, Friedman KD, Gill JC, Morateck PA, Wren JS, Scott JP, Montgomery RR) J Thromb Haemost 2009 Nov;7(11):1832-9 PMID: 19694940 PMCID: PMC3825106 SCOPUS ID: 2-s2.0-70449436494 08/22/2009       75 Citations
  • Leukocyte proteases cleave von Willebrand factor at or near the ADAMTS13 cleavage site. (Raife TJ, Cao W, Atkinson BS, Bedell B, Montgomery RR, Lentz SR, Johnson GF, Zheng XL) Blood 2009 Aug 20;114(8):1666-74 PMID: 19541819 PMCID: PMC2731642 SCOPUS ID: 2-s2.0-70349569566 06/23/2009       109 Citations
  • Clinical and laboratory diagnosis of von Willebrand disease: a synopsis of the 2008 NHLBI/NIH guidelines. (Nichols WL, Rick ME, Ortel TL, Montgomery RR, Sadler JE, Yawn BP, James AH, Hultin MB, Manco-Johnson MJ, Weinstein M) Am J Hematol 2009 Jun;84(6):366-70 PMID: 19415721 PMCID: PMC5592788 SCOPUS ID: 2-s2.0-66849122217 05/06/2009       83 Citations
  • Genetic alteration of the D2 domain abolishes von Willebrand factor multimerization and trafficking into storage. (Haberichter SL, Allmann AM, Jozwiak MA, Montgomery RR, Gill JC) J Thromb Haemost 2009 Apr;7(4):641-50 PMID: 19192112 PMCID: PMC2745278 SCOPUS ID: 2-s2.0-63049092852 02/05/2009       25 Citations
  • At least type VWD2B is a discrete variant of VWD, isn't it? (Montgomery RR) Blood 2009 Jan 15;113(3):501 PMID: 19147792 PMCID: PMC2628358 SCOPUS ID: 2-s2.0-61849098294 01/17/2009       2 Citations
  • von Willebrand factor content in Alphanate® (Laurence J. Logan) - Reply (Nichols WL, Hultln MB, James AH, Manco-johnson MJ, Montgomery RR, Ortel TL, Rick ME, Sadler JE, Weinstein M, Yawn BP) Haemophilia January 2009;15(1):370-371 SCOPUS ID: 2-s2.0-63049120238 01/01/2009    
  • von Willebrand factor content in Alphanate(R) (Laurence J. Logan) - reply. (Nichols WL et al.) Haemophilia 2009 Jan 1;15(1):370-371 PMID: 18811592 09/25/2008    
  • Type 2B von Willebrand disease associated with the release of platelet agglutinates from megakaryocytes in the bone marrow. (Slayton WB, Patel M, Sola-Visner M, Harris N, Rivers A, Montgomery RR, Friedman KD) J Pediatr Hematol Oncol 2008 Sep;30(9):708-11 PMID: 18776767 PMCID: PMC5592795 SCOPUS ID: 2-s2.0-65349161369 09/09/2008       7 Citations
  • Syngeneic transplantation of hematopoietic stem cells that are genetically modified to express factor VIII in platelets restores hemostasis to hemophilia A mice with preexisting FVIII immunity. (Shi Q, Fahs SA, Wilcox DA, Kuether EL, Morateck PA, Mareno N, Weiler H, Montgomery RR) Blood 2008 Oct 01;112(7):2713-21 PMID: 18495954 PMCID: PMC2556608 SCOPUS ID: 2-s2.0-53449090226 05/23/2008       89 Citations
  • Identification of type 1 von Willebrand disease patients with reduced von Willebrand factor survival by assay of the VWF propeptide in the European study: molecular and clinical markers for the diagnosis and management of type 1 VWD (MCMDM-1VWD). (Haberichter SL, Castaman G, Budde U, Peake I, Goodeve A, Rodeghiero F, Federici AB, Batlle J, Meyer D, Mazurier C, Goudemand J, Eikenboom J, Schneppenheim R, Ingerslev J, Vorlova Z, Habart D, Holmberg L, Lethagen S, Pasi J, Hill FG, Montgomery RR) Blood 2008 May 15;111(10):4979-85 PMID: 18344424 PMCID: PMC2384129 SCOPUS ID: 2-s2.0-46749133213 03/18/2008       155 Citations
  • von Willebrand disease (VWD): evidence-based diagnosis and management guidelines, the National Heart, Lung, and Blood Institute (NHLBI) Expert Panel report (USA). (Nichols WL, Hultin MB, James AH, Manco-Johnson MJ, Montgomery RR, Ortel TL, Rick ME, Sadler JE, Weinstein M, Yawn BP) Haemophilia 2008 Mar;14(2):171-232 PMID: 18315614 SCOPUS ID: 2-s2.0-83055187115 03/05/2008       831 Citations
  • β2-GPI dampening of VWF-GPIb interaction (Montgomery RR) Blood 1 September 2007;110(5):1405 SCOPUS ID: 2-s2.0-34548843336 09/01/2007    
  • Lentivirus-mediated platelet-derived factor VIII gene therapy in murine haemophilia A. (Shi Q, Wilcox DA, Fahs SA, Fang J, Johnson BD, DU LM, Desai D, Montgomery RR) J Thromb Haemost 2007 Feb;5(2):352-61 PMID: 17269937 SCOPUS ID: 2-s2.0-33846453333 02/03/2007       124 Citations
  • Mouse VWF again teaches us diversity of mechanisms (Montgomery RR) Blood 1 November 2006;108(9):2887 SCOPUS ID: 2-s2.0-33751198275 11/01/2006    
  • When it comes to von Willebrand disease, does 1 + 1 = 3? (Montgomery RR) J Thromb Haemost 2006 Oct;4(10):2162-3 PMID: 16889558 SCOPUS ID: 2-s2.0-33748749084 08/08/2006       6 Citations
  • Update on the pathophysiology and classification of von Willebrand disease: a report of the Subcommittee on von Willebrand Factor. (Sadler JE, Budde U, Eikenboom JC, Favaloro EJ, Hill FG, Holmberg L, Ingerslev J, Lee CA, Lillicrap D, Mannucci PM, Mazurier C, Meyer D, Nichols WL, Nishino M, Peake IR, Rodeghiero F, Schneppenheim R, Ruggeri ZM, Srivastava A, Montgomery RR, Federici AB, Working Party on von Willebrand Disease Classification) J Thromb Haemost 2006 Oct;4(10):2103-14 PMID: 16889557 SCOPUS ID: 2-s2.0-33748802581 08/08/2006       1061 Citations
  • Assay of the von Willebrand factor (VWF) propeptide to identify patients with type 1 von Willebrand disease with decreased VWF survival. (Haberichter SL, Balistreri M, Christopherson P, Morateck P, Gavazova S, Bellissimo DB, Manco-Johnson MJ, Gill JC, Montgomery RR) Blood 2006 Nov 15;108(10):3344-51 PMID: 16835381 PMCID: PMC1895439 SCOPUS ID: 2-s2.0-33751013939 07/13/2006       187 Citations
  • Factor VIII ectopically targeted to platelets is therapeutic in hemophilia A with high-titer inhibitory antibodies. (Shi Q, Wilcox DA, Fahs SA, Weiler H, Wells CW, Cooley BC, Desai D, Morateck PA, Gorski J, Montgomery RR) J Clin Invest 2006 Jul;116(7):1974-82 PMID: 16823491 PMCID: PMC1483176 SCOPUS ID: 2-s2.0-33745864802 07/11/2006       164 Citations
  • A package for VWD endothelial cells (Montgomery RR) Blood 15 June 2006;107(12):4580-4581 SCOPUS ID: 2-s2.0-33745091219 06/15/2006       1 Citation
  • More on: are randomized clinical trials the only truth? Not always. (Medical and Scientific Advisory Council, National Hemophilia Foundation) J Thromb Haemost 2006 May;4(5):1167-8 PMID: 16689784 SCOPUS ID: 2-s2.0-33645643112 05/13/2006       9 Citations
  • Regulated release of VWF and FVIII and the biologic implications. (Haberichter SL, Shi Q, Montgomery RR) Pediatr Blood Cancer 2006 May 01;46(5):547-53 PMID: 16470522 SCOPUS ID: 2-s2.0-33645304827 02/14/2006       47 Citations
  • von Willebrand disease--the relevance of history. (Montgomery RR) J Thromb Haemost 2005 Dec;3(12):2617-8 PMID: 16359501 SCOPUS ID: 2-s2.0-29244478325 12/20/2005       7 Citations
  • Genetic mutations in von Willebrand disease identified by DHPLC and DNA sequence analysis. (Kakela JK, Friedman KD, Haberichter SL, Buchholz NP, Christopherson PA, Kroner PA, Gill JC, Montgomery RR, Bellissimo DB) Mol Genet Metab 2006 Mar;87(3):262-71 PMID: 16321553 SCOPUS ID: 2-s2.0-33644662851 12/03/2005       15 Citations
  • von Willebrand factor: the new treatment paradigm--introduction. (Lee CA, Montgomery RR) Blood Coagul Fibrinolysis 2005 Apr;16 Suppl 1:S1-2 PMID: 15849520 SCOPUS ID: 2-s2.0-19944362489 04/26/2005    
  • Intracellular interaction of von Willebrand factor and factor VIII depends on cellular context: lessons from platelet-expressed factor VIII. (Yarovoi H, Nurden AT, Montgomery RR, Nurden P, Poncz M) Blood 2005 Jun 15;105(12):4674-6 PMID: 15731176 SCOPUS ID: 2-s2.0-20444417088 02/26/2005       33 Citations
  • Targeting platelet GPIbalpha transgene expression to human megakaryocytes and forming a complete complex with endogenous GPIbbeta and GPIX. (Shi Q, Wilcox DA, Morateck PA, Fahs SA, Kenny D, Montgomery RR) J Thromb Haemost 2004 Nov;2(11):1989-97 PMID: 15550031 SCOPUS ID: 2-s2.0-13244262627 11/20/2004       33 Citations
  • Re-establishment of VWF-dependent Weibel-Palade bodies in VWD endothelial cells. (Haberichter SL, Merricks EP, Fahs SA, Christopherson PA, Nichols TC, Montgomery RR) Blood 2005 Jan 01;105(1):145-52 PMID: 15331450 PMCID: PMC3938105 SCOPUS ID: 2-s2.0-11144247649 08/28/2004       63 Citations
  • Severe deficiency of VWF-cleaving protease (ADAMTS13) activity defines a distinct population of thrombotic microangiopathy patients. (Raife T, Atkinson B, Montgomery R, Vesely S, Friedman K) Transfusion 2004 Feb;44(2):146-50 PMID: 14962303 SCOPUS ID: 2-s2.0-1242344743 02/14/2004       75 Citations
  • Induction of megakaryocytes to synthesize and store a releasable pool of human factor VIII. (Wilcox DA, Shi Q, Nurden P, Haberichter SL, Rosenberg JB, Johnson BD, Nurden AT, White GC 2nd, Montgomery RR) J Thromb Haemost 2003 Dec;1(12):2477-89 PMID: 14675082 SCOPUS ID: 2-s2.0-1542544992 12/17/2003       56 Citations
  • PECAM-1 negatively regulates GPIb/V/IX signaling in murine platelets. (Rathore V, Stapleton MA, Hillery CA, Montgomery RR, Nichols TC, Merricks EP, Newman DK, Newman PJ) Blood 2003 Nov 15;102(10):3658-64 PMID: 12893757 SCOPUS ID: 2-s2.0-0242411524 08/02/2003       79 Citations
  • Factor VIII ectopically expressed in platelets: efficacy in hemophilia A treatment. (Yarovoi HV, Kufrin D, Eslin DE, Thornton MA, Haberichter SL, Shi Q, Zhu H, Camire R, Fakharzadeh SS, Kowalska MA, Wilcox DA, Sachais BS, Montgomery RR, Poncz M) Blood 2003 Dec 01;102(12):4006-13 PMID: 12881300 SCOPUS ID: 2-s2.0-10744231807 07/26/2003       137 Citations
  • Expression of human factor VIII under control of the platelet-specific alphaIIb promoter in megakaryocytic cell line as well as storage together with VWF. (Shi Q, Wilcox DA, Fahs SA, Kroner PA, Montgomery RR) Mol Genet Metab 2003 May;79(1):25-33 PMID: 12765843 SCOPUS ID: 2-s2.0-0038522536 05/27/2003       46 Citations
  • Comparative response of plasma VWF in dogs to up-regulation of VWF mRNA by interleukin-11 versus Weibel-Palade body release by desmopressin (DDAVP). (Olsen EH, McCain AS, Merricks EP, Fischer TH, Dillon IM, Raymer RA, Bellinger DA, Fahs SA, Montgomery RR, Keith JC Jr, Schaub RG, Nichols TC) Blood 2003 Jul 15;102(2):436-41 PMID: 12649145 SCOPUS ID: 2-s2.0-0037818706 03/22/2003       32 Citations
  • Critical independent regions in the VWF propeptide and mature VWF that enable normal VWF storage. (Haberichter SL, Jacobi P, Montgomery RR) Blood 2003 Feb 15;101(4):1384-91 PMID: 12393513 SCOPUS ID: 2-s2.0-0037441597 10/24/2002       49 Citations
  • The role of the D1 domain of the von Willebrand factor propeptide in multimerization of VWF. (Rosenberg JB, Haberichter SL, Jozwiak MA, Vokac EA, Kroner PA, Fahs SA, Kawai Y, Montgomery RR) Blood 2002 Sep 01;100(5):1699-706 PMID: 12176890 SCOPUS ID: 2-s2.0-0036721163 08/15/2002       57 Citations
  • The von Willebrand factor propeptide (VWFpp) traffics an unrelated protein to storage. (Haberichter SL, Jozwiak MA, Rosenberg JB, Christopherson PA, Montgomery RR) Arterioscler Thromb Vasc Biol 2002 Jun 01;22(6):921-6 PMID: 12067899 SCOPUS ID: 2-s2.0-0036075304 06/18/2002       40 Citations
  • The cysteine knot of platelet glycoprotein Ib beta (GPIb beta) is critical for the interaction of GPIb beta with GPIX. (Kenny D, Morateck PA, Montgomery RR) Blood 2002 Jun 15;99(12):4428-33 PMID: 12036872 SCOPUS ID: 2-s2.0-0037097592 05/31/2002       18 Citations
  • New aspects in the pathogenesis and treatment of thrombotic thrombocytopenic purpura and hemolytic uremic syndrome. (Raife T, Montgomery R) Rev Clin Exp Hematol 2001 Sep;5(3):236-61; discussion 311-2 PMID: 11703817 SCOPUS ID: 2-s2.0-0035467604 11/13/2001       15 Citations
  • von Willebrand disease: a common pediatric disorder. (Montgomery RR, Kroner PA) Pediatr Ann 2001 Sep;30(9):534-40 PMID: 11554262 SCOPUS ID: 2-s2.0-0034748514 09/14/2001       12 Citations
  • Bleeding disorders: A common cause of menorrhagia in adolescents. (Bevan JA, Maloney KW, Hillery CA, Gill JC, Montgomery RR, Scott JP) J Pediatr 2001 Jun;138(6):856-61 PMID: 11391329 SCOPUS ID: 2-s2.0-0034971466 06/08/2001       154 Citations
  • Genetic induction of a releasable pool of factor VIII in human endothelial cells. (Rosenberg JB, Greengard JS, Montgomery RR) Arterioscler Thromb Vasc Biol 2000 Dec;20(12):2689-95 PMID: 11116073 SCOPUS ID: 2-s2.0-0033669966 12/16/2000       72 Citations
  • von Willebrand factor storage and multimerization: 2 independent intracellular processes. (Haberichter SL, Fahs SA, Montgomery RR) Blood 2000 Sep 01;96(5):1808-15 PMID: 10961880 SCOPUS ID: 2-s2.0-0034284294 08/29/2000       76 Citations
  • von Willebrand factor and thrombotic thrombocytopenic purpura. (Raife TJ, Montgomery RR) Curr Opin Hematol 2000 Sep;7(5):278-83 PMID: 10961577 SCOPUS ID: 2-s2.0-0033883648 08/29/2000       11 Citations
  • Surface expression of glycoprotein ib alpha is dependent on glycoprotein ib beta: evidence from a novel mutation causing Bernard-Soulier syndrome. (Moran N, Morateck PA, Deering A, Ryan M, Montgomery RR, Fitzgerald DJ, Kenny D) Blood 2000 Jul 15;96(2):532-9 PMID: 10887115 SCOPUS ID: 2-s2.0-0034661909 07/11/2000       59 Citations
  • Interactions between von Willebrand factor and Factor VIII: where did they first meet. (Montgomery RR, Gill JC) J Pediatr Hematol Oncol 2000;22(3):269-75 PMID: 10864063 SCOPUS ID: 2-s2.0-0034455182 06/23/2000       35 Citations
  • Low-molecular-weight heparin in thrombotic disease in children and adolescents. (Punzalan RC, Hillery CA, Montgomery RR, Scott CA, Gill JC) J Pediatr Hematol Oncol 2000;22(2):137-42 PMID: 10779027 SCOPUS ID: 2-s2.0-0034456438 04/25/2000       76 Citations
  • Cloning and expression of canine glycoprotein Ibalpha. (Kenny D, Morateck PA, Fahs SA, Warltier DC, Montgomery RR) Thromb Haemost 1999 Oct;82(4):1327-33 PMID: 10544923 SCOPUS ID: 2-s2.0-0032827491 11/02/1999       8 Citations
  • Contribution of the glycoprotein Ia 807TT, methylene tetrahydrofolate reductase 677TT and prothrombin 20210GA genotypes to prothrombotic risk among factor V 1691GA (Leiden) carriers. (Hessner MJ, Dinauer DM, Luhm RA, Endres JL, Montgomery RR, Friedman KD) Br J Haematol 1999 Jul;106(1):237-9 PMID: 10444193 SCOPUS ID: 2-s2.0-0032838868 08/12/1999       15 Citations
  • Prevalence of prothrombin G20210A, factor V G1691A (Leiden), and methylenetetrahydrofolate reductase (MTHFR) C677T in seven different populations determined by multiplex allele-specific PCR. (Hessner MJ, Luhm RA, Pearson SL, Endean DJ, Friedman KD, Montgomery RR) Thromb Haemost 1999 May;81(5):733-8 PMID: 10365746 SCOPUS ID: 2-s2.0-0032933161 06/12/1999       128 Citations
  • The critical interaction of glycoprotein (GP) IBbeta with GPIX-a genetic cause of Bernard-Soulier syndrome. (Kenny D, Morateck PA, Gill JC, Montgomery RR) Blood 1999 May 01;93(9):2968-75 PMID: 10216092 SCOPUS ID: 2-s2.0-0033135652 04/27/1999       68 Citations
  • Naturally occurring mutations in glycoprotein Ibalpha that result in defective ligand binding and synthesis of a truncated protein. (Kenny D, Jónsson OG, Morateck PA, Montgomery RR) Blood 1998 Jul 01;92(1):175-83 PMID: 9639514 SCOPUS ID: 2-s2.0-2642625659 06/25/1998       47 Citations
  • Intracellular trafficking of factor VIII to von Willebrand factor storage granules. (Rosenberg JB, Foster PA, Kaufman RJ, Vokac EA, Moussalli M, Kroner PA, Montgomery RR) J Clin Invest 1998 Feb 01;101(3):613-24 PMID: 9449695 PMCID: PMC508605 SCOPUS ID: 2-s2.0-0032007271 03/21/1998       109 Citations
  • Type 2M von Willebrand disease: F606I and I662F mutations in the glycoprotein Ib binding domain selectively impair ristocetin- but not botrocetin-mediated binding of von Willebrand factor to platelets. (Hillery CA, Mancuso DJ, Evan Sadler J, Ponder JW, Jozwiak MA, Christopherson PA, Cox Gill J, Paul Scott J, Montgomery RR) Blood 1998 Mar 01;91(5):1572-81 PMID: 9473222 SCOPUS ID: 2-s2.0-0032032301 03/21/1998       90 Citations
  • A dinucleotide deletion results in defective membrane anchoring and circulating soluble glycoprotein Ib alpha in a novel form of Bernard-Soulier syndrome. (Kenny D, Newman PJ, Morateck PA, Montgomery RR) Blood 1997 Oct 01;90(7):2626-33 PMID: 9326229 SCOPUS ID: 2-s2.0-0030794862 11/05/1997       34 Citations
  • Interaction of von Willebrand factor with Staphylococcus aureus. (Herrmann M, Hartleib J, Kehrel B, Montgomery RR, Sixma JJ, Peters G) J Infect Dis 1997 Oct;176(4):984-91 PMID: 9333157 SCOPUS ID: 2-s2.0-0030763918 10/23/1997       69 Citations
  • Type 2M:Milwaukee-1 von Willebrand disease: an in-frame deletion in the Cys509-Cys695 loop of the von Willebrand factor A1 domain causes deficient binding of von Willebrand factor to platelets. (Mancuso DJ, Kroner PA, Christopherson PA, Vokac EA, Gill JC, Montgomery RR) Blood 1996 Oct 01;88(7):2559-68 PMID: 8839848 SCOPUS ID: 2-s2.0-0029796142 10/01/1996       64 Citations
  • Pharmacokinetics of von Willebrand factor and factor VIIIC in patients with severe von Willebrand disease (type 3 VWD): estimation of the rate of factor VIIIC synthesis. Cooperative Study Groups. (Menache D, Aronson DL, Darr F, Montgomery RR, Gill JC, Kessler CM, Lusher JM, Phatak PD, Shapiro AD, Thompson AR, White GC 2nd) Br J Haematol 1996 Sep;94(4):740-5 PMID: 8826903 SCOPUS ID: 2-s2.0-9544220778 09/01/1996       62 Citations
  • Increased adhesion of erythrocytes to components of the extracellular matrix: isolation and characterization of a red blood cell lipid that binds thrombospondin and laminin. (Hillery CA, Du MC, Montgomery RR, Scott JP) Blood 1996 Jun 01;87(11):4879-86 PMID: 8639862 SCOPUS ID: 2-s2.0-0029897658 06/01/1996       134 Citations
  • Inhibition of platelet adhesion to collagen by monoclonal anti-CD36 antibodies. (Matsuno K, Diaz-Ricart M, Montgomery RR, Aster RH, Jamieson GA, Tandon NN) Br J Haematol 1996 Mar;92(4):960-7 PMID: 8616094 SCOPUS ID: 2-s2.0-0029878896 03/01/1996       60 Citations
  • The defective interaction between von Willebrand factor and factor VIII in a patient with type 1 von Willebrand disease is caused by substitution of Arg19 and His54 in mature von Willebrand factor. (Kroner PA, Foster PA, Fahs SA, Montgomery RR) Blood 1996 Feb 01;87(3):1013-21 PMID: 8562925 SCOPUS ID: 2-s2.0-0030040896 02/01/1996       56 Citations
  • Direct demonstration of antigenic substitution of Borrelia burgdorferi ex vivo: exploration of the paradox of the early immune response to outer surface proteins A and C in Lyme disease. (Montgomery RR, Malawista SE, Feen KJ, Bockenstedt LK) J Exp Med 1996 Jan 01;183(1):261-9 PMID: 8551229 PMCID: PMC2192432 SCOPUS ID: 2-s2.0-0030048119 01/01/1996       184 Citations
  • Panel discussion on the development of inhibitors: Who and why? (White GC, Briet E, Gilles JGG, Hoyer LW, Kazatchkine M, Montgomery RR, Preston FE, Reisner HM, Aledort LM, Aronson D, Goodnow C, Jenkins M, Kay M, Monroe DM, Scandella D, Scott DW) Advances in Experimental Medicine and Biology 1995;386:235-246 SCOPUS ID: 2-s2.0-0029555755 12/01/1995    
  • Panel discussion on the treatment of inhibitors: Today and tomorrow (Hilgartner MW, Aledort LM, Brackmann HH, Kasper CK, Lusher JM, Rickles FR, Scott DW, Alderman E, Gill J, Gilles JGG, Jenkins M, Kazatchkine M, Mariani G, Montgomery R, Nilsson IM, Preston FE, Reisner HM, White GC) Advances in Experimental Medicine and Biology 1995;386:247-262 SCOPUS ID: 2-s2.0-0029554224 12/01/1995    
  • Comparison of six commercial plasma references for factor VIII, factor IX and von Willebrand factor. On behalf of the Subcommittee for Factor VIII and IX of the Scientific and Standardization Committee of the ISTH. (Kasper CK, Aronson DL, Davignon G, Foster P, Hillman-Wiseman C, Lusher JM, Manco-Johnson M, Meade JB, Montgomery RR, Rickles FR) Thromb Haemost 1995 Sep;74(3):987-9 PMID: 8571334 SCOPUS ID: 2-s2.0-0029082911 09/01/1995       7 Citations
  • Cultured endothelial cells restore vasodilator responses to coronary arteries with impaired endothelial function and alter the response to a nitric oxide donor. (Kenny D, Coughlan MG, Kampine JP, Montgomery RR, Bosnjak ZJ, Warltier DC) Pharmacology 1994 Oct;49(4):249-56 PMID: 7831388 SCOPUS ID: 2-s2.0-0028050348 10/01/1994       3 Citations
  • Fc- and non-Fc-mediated phagocytosis of Borrelia burgdorferi by macrophages. (Montgomery RR, Nathanson MH, Malawista SE) J Infect Dis 1994 Oct;170(4):890-3 PMID: 7930732 SCOPUS ID: 2-s2.0-0028086479 10/01/1994       43 Citations
  • Relative antithrombotic effects of monoclonal antibodies targeting different platelet glycoprotein-adhesive molecule interactions in nonhuman primates. (Cadroy Y, Hanson SR, Kelly AB, Marzec UM, Evatt BL, Kunicki TJ, Montgomery RR, Harker LA) Blood 1994 Jun 01;83(11):3218-24 PMID: 8193356 SCOPUS ID: 2-s2.0-0028361191 06/01/1994       70 Citations
  • Genetic mutations in ten unrelated American patients with symptomatic type 1 protein C deficiency. (Tsay W, Greengard JS, Montgomery RR, McPherson RA, Fucci JC, Koerper MA, Coughlin J, Griffin JH) Blood Coagul Fibrinolysis 1993 Oct;4(5):791-6 PMID: 8292730 SCOPUS ID: 2-s2.0-0027520670 10/01/1993       20 Citations
  • Therapy of von Willebrand disease. (Scott JP, Montgomery RR) Semin Thromb Hemost 1993;19(1):37-47 PMID: 8456322 SCOPUS ID: 2-s2.0-0027411862 01/01/1993       42 Citations
  • Multiple coagulation factor abnormalities in commercially available Passovoy-deficient plasma. (Foster PA, Montgomery RR, Endres-Brooks J) Blood 1992 Dec 15;80(12):3260-1 PMID: 1467533 SCOPUS ID: 2-s2.0-0027092061 12/15/1992       3 Citations
  • Protein C survival during replacement therapy in homozygous protein C deficiency. (Marlar RA, Sills RH, Groncy PK, Montgomery RR, Madden RM) Am J Hematol 1992 Sep;41(1):24-31 PMID: 1503096 SCOPUS ID: 2-s2.0-0026701101 09/01/1992       28 Citations
  • Expressed full-length von Willebrand factor containing missense mutations linked to type IIB von Willebrand disease shows enhanced binding to platelets. (Kroner PA, Kluessendorf ML, Scott JP, Montgomery RR) Blood 1992 Apr 15;79(8):2048-55 PMID: 1373334 SCOPUS ID: 2-s2.0-0026700987 04/15/1992       56 Citations
  • Fine mapping of monoclonal antibody epitopes on human von Willebrand factor using a recombinant peptide library. (Ginsburg D, Bockenstedt PL, Allen EA, Fox DA, Foster PA, Ruggeri ZM, Zimmerman TS, Montgomery RR, Bahou WF, Johnson TA) Thromb Haemost 1992 Jan 23;67(1):166-71 PMID: 1377414 SCOPUS ID: 2-s2.0-0026508968 01/23/1992       20 Citations
  • The rapid differentiation of type IIb von Willebrand's disease from platelet-type (pseudo-) von Willebrand's disease by the "neutral" monoclonal antibody binding assay. (Scott JP, Montgomery RR) Am J Clin Pathol 1991 Dec;96(6):723-8 PMID: 1746488 SCOPUS ID: 2-s2.0-0026323814 12/01/1991       34 Citations
  • Accumulation of indigestible substances reduces fusion competence of macrophage lysosomes. (Montgomery RR, Webster P, Mellman I) J Immunol 1991 Nov 01;147(9):3087-95 PMID: 1919007 SCOPUS ID: 2-s2.0-0026077258 11/01/1991       53 Citations
  • Abnormal binding of factor VIII is linked with the substitution of glutamine for arginine 91 in von Willebrand factor in a variant form of von Willebrand disease. (Kroner PA, Friedman KD, Fahs SA, Scott JP, Montgomery RR) J Biol Chem 1991 Oct 15;266(29):19146-9 PMID: 1918030 SCOPUS ID: 2-s2.0-0026002404 10/15/1991       74 Citations
  • Dimeric ristocetin flocculates proteins, binds to platelets, and mediates von Willebrand factor-dependent agglutination of platelets. (Scott JP, Montgomery RR, Retzinger GS) J Biol Chem 1991 May 05;266(13):8149-55 PMID: 2022635 SCOPUS ID: 2-s2.0-0025901142 05/05/1991       132 Citations
  • Evaluation of merocyanine 540-sensitized photoirradiation as a means to inactivate enveloped viruses in blood products. (O'Brien JM, Montgomery RR, Burns WH, Gaffney DK, Sieber F) J Lab Clin Med 1990 Oct;116(4):439-47 PMID: 2170551 SCOPUS ID: 2-s2.0-44949287038 10/01/1990       61 Citations
  • Report on the diagnosis and treatment of homozygous protein C deficiency. Report of the Working Party on Homozygous Protein C Deficiency of the ICTH-Subcommittee on Protein C and Protein S. (Marlar RA, Montgomery RR, Broekmans AW) Thromb Haemost 1989 Jun 30;61(3):529-31 PMID: 2529664 SCOPUS ID: 2-s2.0-0024399901 06/30/1989       50 Citations
  • Molecular basis of human von Willebrand disease: analysis of platelet von Willebrand factor mRNA. (Ginsburg D, Konkle BA, Gill JC, Montgomery RR, Bockenstedt PL, Johnson TA, Yang AY) Proc Natl Acad Sci U S A 1989 May;86(10):3723-7 PMID: 2786201 PMCID: PMC287212 SCOPUS ID: 2-s2.0-0024669945 05/01/1989       132 Citations
  • Diagnosis and treatment of homozygous protein C deficiency. Report of the Working Party on Homozygous Protein C Deficiency of the Subcommittee on Protein C and Protein S, International Committee on Thrombosis and Haemostasis. (Marlar RA, Montgomery RR, Broekmans AW) J Pediatr 1989 Apr;114(4 Pt 1):528-34 PMID: 2647943 SCOPUS ID: 2-s2.0-0024603102 04/01/1989       194 Citations
  • Endocytic and secretory repertoire of the lipid-loaded macrophage. (Montgomery RR, Cohn ZA) J Leukoc Biol 1989 Feb;45(2):129-38 PMID: 2492592 SCOPUS ID: 2-s2.0-0024500409 02/01/1989       26 Citations
  • Enzymatic amplification of specific cDNA inserts from lambda gt11 libraries. (Friedman KD, Rosen NL, Newman PJ, Montgomery RR) Nucleic Acids Res 1988 Sep 12;16(17):8718 PMID: 2843825 PMCID: PMC338596 SCOPUS ID: 2-s2.0-0023758387 09/12/1988       47 Citations
  • Homozygous protein C deficiency: observations on the nature of the molecular abnormality and the effectiveness of warfarin therapy. (Peters C, Casella JF, Marlar RA, Montgomery RR, Zinkham WH) Pediatrics 1988 Feb;81(2):272-6 PMID: 3340476 SCOPUS ID: 2-s2.0-0023911084 02/01/1988       29 Citations
  • Effects of monoclonal antibodies against the platelet glycoprotein IIb/IIIa complex on thrombosis and hemostasis in the baboon. (Hanson SR, Pareti FI, Ruggeri ZM, Marzec UM, Kunicki TJ, Montgomery RR, Zimmerman TS, Harker LA) J Clin Invest 1988 Jan;81(1):149-58 PMID: 2961790 PMCID: PMC442486 SCOPUS ID: 2-s2.0-0023877450 01/01/1988       135 Citations
  • Low-dose aspirin protects against lipid accumulation in primate vein bypass grafts. (Boerboom LE, Olinger GN, Kissebah AH, Montgomery RR) J Thorac Cardiovasc Surg 1987 Aug;94(2):251-5 PMID: 3613624 SCOPUS ID: 2-s2.0-0023248854 08/01/1987       8 Citations
  • The effect of ABO blood group on the diagnosis of von Willebrand disease. (Gill JC, Endres-Brooks J, Bauer PJ, Marks WJ Jr, Montgomery RR) Blood 1987 Jun;69(6):1691-5 PMID: 3495304 SCOPUS ID: 2-s2.0-0023257218 06/01/1987       855 Citations
  • Protein C deficiency. (Rappaport ES, Speights VO, Helbert B, Trowbridge A, Koops B, Montgomery RR, Marlar RA) South Med J 1987 Feb;80(2):240-2 PMID: 3810223 SCOPUS ID: 2-s2.0-0023293528 02/01/1987       19 Citations
  • Endothelial cell processing of von Willebrand proteins. (Kawai Y, Montgomery RR) Ann N Y Acad Sci 1987;509:60-70 PMID: 3122620 SCOPUS ID: 2-s2.0-0023633565 01/01/1987       18 Citations
  • Effects of reagent and cell-generated hydrogen peroxide on the properties of low density lipoprotein. (Montgomery RR, Nathan CF, Cohn ZA) Proc Natl Acad Sci U S A 1986 Sep;83(17):6631-5 PMID: 3018740 PMCID: PMC386558 SCOPUS ID: 2-s2.0-0023018813 09/01/1986       20 Citations
  • Synthesis by cultured human umbilical vein endothelial cells of two proteins structurally and immunologically related to platelet membrane glycoproteins IIb and IIIa. (Newman PJ, Kawai Y, Montgomery RR, Kunicki TJ) J Cell Biol 1986 Jul;103(1):81-6 PMID: 2941443 PMCID: PMC2113805 SCOPUS ID: 2-s2.0-0022474387 07/01/1986       39 Citations
  • Propolypeptide of von Willebrand factor circulates in blood and is identical to von Willebrand antigen II. (Fay PJ, Kawai Y, Wagner DD, Ginsburg D, Bonthron D, Ohlsson-Wilhelm BM, Chavin SI, Abraham GN, Handin RI, Orkin SH) Science 1986 May 23;232(4753):995-8 PMID: 3486471 SCOPUS ID: 2-s2.0-0022456315 05/23/1986       104 Citations
  • HTLV-III serology in hemophilia: relationship with immunologic abnormalities. (Gill JC, Menitove JE, Anderson PR, Casper JT, Devare SG, Wood C, Adair S, Casey J, Scheffel C, Montgomery RR) J Pediatr 1986 Apr;108(4):511-6 PMID: 3083075 SCOPUS ID: 2-s2.0-0022619581 04/01/1986       13 Citations
  • Loss of the largest von Willebrand factor multimers from the plasma of patients with congenital cardiac defects. (Gill JC, Wilson AD, Endres-Brooks J, Montgomery RR) Blood 1986 Mar;67(3):758-61 PMID: 3484979 SCOPUS ID: 2-s2.0-0022597036 03/01/1986       213 Citations
  • Use of monoclonal antibody to increase the sensitivity and specificity of precipitating immunoassays and cell surface binding immunoassays. (Montgomery RR, Kunicki TJ, Glode LM) Methods Enzymol 1986;121:702-17 PMID: 3724493 SCOPUS ID: 2-s2.0-0022556057 01/01/1986       10 Citations
  • Inherited absence of OKT4 lymphocyte antigen in a chronically transfused patient with homozygous sickle cell disease. (Gill JC, Maples J, Nikaein A, Kirchner P, Lockhart D, Snyder AJ, Montgomery RR, Casper JT) J Pediatr 1985 Aug;107(2):251-3 PMID: 3874945 SCOPUS ID: 2-s2.0-0022392208 08/01/1985       1 Citation
  • Persistence and progression of immunologic abnormalities in haemophilia. (Gill JC, Wheeler D, Menitove JE, Aster RH, Casper JT, Kirchner P, Montgomery RR) Thromb Haemost 1985 Jun 24;53(3):328-31 PMID: 3931282 SCOPUS ID: 2-s2.0-0021878480 06/24/1985       1 Citation
  • Newborn haemostasis. (Montgomery RR, Marlar RA, Gill JC) Clin Haematol 1985 Jun;14(2):443-60 PMID: 3899442 SCOPUS ID: 2-s2.0-0021891210 06/01/1985       26 Citations
  • Endothelial cell synthesis of von Willebrand antigen II, von Willebrand factor, and von Willebrand factor/von Willebrand antigen II complex. (McCarroll DR, Levin EG, Montgomery RR) J Clin Invest 1985 Apr;75(4):1089-95 PMID: 3872883 PMCID: PMC425431 SCOPUS ID: 2-s2.0-0021994485 04/01/1985       41 Citations
  • Cleavage of human von Willebrand factor by platelet calcium-activated protease. (Kunicki TJ, Montgomery RR, Schullek J) Blood 1985 Feb;65(2):352-6 PMID: 2981585 SCOPUS ID: 2-s2.0-0021959235 02/01/1985       69 Citations
  • On the association of glycoprotein Ib and actin-binding protein in human platelets. (Okita JR, Pidard D, Newman PJ, Montgomery RR, Kunicki TJ) J Cell Biol 1985 Jan;100(1):317-21 PMID: 3155520 PMCID: PMC2113466 SCOPUS ID: 2-s2.0-0021912911 01/01/1985       134 Citations
  • Comparison of the sensitivity of commercial APTT reagents in the detection of mild coagulopathies. (Marlar RA, Bauer PJ, Endres-Brooks JL, Montgomery RR, Miller CM, Schanen MM) Am J Clin Pathol 1984 Oct;82(4):436-9 PMID: 6475840 SCOPUS ID: 2-s2.0-0021137174 10/01/1984       27 Citations
  • Severe homozygous protein C deficiency. (Sills RH, Marlar RA, Montgomery RR, Deshpande GN, Humbert JR) J Pediatr 1984 Sep;105(3):409-13 PMID: 6547978 SCOPUS ID: 2-s2.0-0021233839 09/01/1984       115 Citations
  • Autoantibodies against platelet glycoprotein Ib in patients with chronic immune thrombocytopenic purpura. (Woods VL Jr, Kurata Y, Montgomery RR, Tani P, Mason D, Oh EH, McMillan R) Blood 1984 Jul;64(1):156-60 PMID: 6234034 SCOPUS ID: 2-s2.0-0021256427 07/01/1984       191 Citations
  • Correlation between circulating levels of von Willebrand's antigen II and von Willebrand factor: discrimination between type I and type II von Willebrand's disease. (McCarroll DR, Ruggeri ZM, Montgomery RR) J Lab Clin Med 1984 May;103(5):704-11 PMID: 6609219 SCOPUS ID: 2-s2.0-0021354080 05/01/1984       22 Citations
  • The effect of DDAVP on plasma levels of von Willebrand antigen II in normal individuals and patients with von Willebrand's disease. (McCarroll DR, Ruggeri ZM, Montgomery RR) Blood 1984 Mar;63(3):532-5 PMID: 6607754 SCOPUS ID: 2-s2.0-0021344581 03/01/1984       21 Citations
  • Interaction of von Willebrand factor with human platelets in the plasma milieu. (Schullek J, Jordan J, Montgomery RR) J Clin Invest 1984 Feb;73(2):421-8 PMID: 6230372 PMCID: PMC425033 SCOPUS ID: 2-s2.0-0021347812 02/01/1984       78 Citations
  • Interaction of AP-2, a monoclonal antibody specific for the human platelet glycoprotein IIb-IIIa complex, with intact platelets. (Pidard D, Montgomery RR, Bennett JS, Kunicki TJ) J Biol Chem 1983 Oct 25;258(20):12582-6 PMID: 6226659 SCOPUS ID: 2-s2.0-0021027332 10/25/1983       268 Citations
  • Platelets have more than one binding site for von Willebrand factor. (Ruggeri ZM, De Marco L, Gatti L, Bader R, Montgomery RR) J Clin Invest 1983 Jul;72(1):1-12 PMID: 6223940 PMCID: PMC1129155 07/01/1983    
  • Generalized lymphadenopathy and T cell abnormalities in hemophilia A. (Gill JC, Menitove JE, Wheeler D, Aster RH, Montgomery RR) J Pediatr 1983 Jul;103(1):18-22 PMID: 6223133 SCOPUS ID: 2-s2.0-0020526898 07/01/1983       39 Citations
  • T-cell subsets in hemophilia. N Engl J Med 1983 May 26;308(21):1291-3 PMID: 6405270 SCOPUS ID: 2-s2.0-85012538035 05/26/1983       33 Citations
  • Prepooled cryoprecipitate for treatment of hemophilia A. (Menitove JE, Spero JA, Richards WA, Lewis JH, Montgomery RR, Gill JC, Hasiba U, Wheeler DV, Sherwin JA, Russell-Vaskov S, Marlar RA, Maxwell NG, Aster RH) Transfusion 1983;23(3):265-7 PMID: 6407160 SCOPUS ID: 2-s2.0-0020527831 05/01/1983       4 Citations
  • Diagnosis of Bernard-Soulier syndrome and Glanzmann's thrombasthenia with a monoclonal assay on whole blood. (Montgomery RR, Kunicki TJ, Taves C, Pidard D, Corcoran M) J Clin Invest 1983 Feb;71(2):385-9 PMID: 6822670 PMCID: PMC436878 02/01/1983    
  • T-lymphocyte subpopulations in patients with classic hemophilia treated with cryoprecipitate and lyophilized concentrates. (Menitove JE, Aster RH, Casper JT, Lauer SJ, Gottschall JL, Williams JE, Gill JC, Wheeler DV, Piaskowski V, Kirchner P, Montgomery RR) N Engl J Med 1983 Jan 13;308(2):83-6 PMID: 6401196 SCOPUS ID: 2-s2.0-0020666179 01/13/1983       224 Citations
  • Diagnosis of Bernard-Soulier syndrome and Glanzmann's thrombasthenia with a monoclonal assay on whole blood (Montgomery RR, Kunicki TJ, Taves C, Pidard D, Corcoran M) Journal of Clinical Investigation 1983;71(2):385-389 SCOPUS ID: 2-s2.0-0020701380 01/01/1983       146 Citations
  • Platelets have more than one binding site for von Willebrand factor (Ruggeri ZM, de Marco L, Gatti L, Bader R, Montgomery RR) Journal of Clinical Investigation 1983;72(1):1-12 SCOPUS ID: 2-s2.0-0020511497 01/01/1983       360 Citations
  • Specific factor VIII-related antigen fragmentation: an in vivo and in vitro phenomenon. (Montgomery RR, Johnson J) Blood 1982 Oct;60(4):930-9 PMID: 6180785 SCOPUS ID: 2-s2.0-0019914175 10/01/1982       31 Citations
  • Influence of high molecular weight factor VIII on the measurement of low molecular weight factor VIII procoagulant in different assay systems. (Muntean W, Hathaway WE, Montgomery RR) Br J Haematol 1982 Aug;51(4):649-58 PMID: 6809034 SCOPUS ID: 2-s2.0-0019943931 08/01/1982       14 Citations
  • A variant of von Willebrand's disease with abnormal expression of factor VIII procoagulant activity. (Montgomery RR, Hathaway WE, Johnson J, Jacobson L, Muntean W) Blood 1982 Jul;60(1):201-7 PMID: 6805535 SCOPUS ID: 2-s2.0-0019947580 07/01/1982       45 Citations
  • Use of monoclonal antibody to increase sensitivity and specificity in quantitative immunodiffusion assays. (Glode LM, Montgomery RR, Smith CG, Link DB) J Immunol Methods 1982;48(1):13-22 PMID: 6799577 SCOPUS ID: 2-s2.0-0020036467 01/01/1982       5 Citations
  • Platelet von Willebrand's antigen II: active release by aggregating agents and a marker of platelet release reaction in vivo. (Scott JP, Montgomery RR) Blood 1981 Dec;58(6):1075-80 PMID: 6975640 SCOPUS ID: 2-s2.0-0019781477 12/01/1981       33 Citations
  • Acquired von Willebrand's disease in association with Wilm's tumor: regression following treatment. (Scott JP, Montgomery RR, Tubergen DG, Hays T) Blood 1981 Oct;58(4):665-9 PMID: 6268230 SCOPUS ID: 2-s2.0-0019418784 10/01/1981       57 Citations
  • Newborn factor VIII complex: elevated activities in term infants and alterations in electrophoretic mobility related to illness and activated coagulation. (Johnson SS, Montgomery RR, Hathaway WE) Br J Haematol 1981 Apr;47(4):597-606 PMID: 6783064 SCOPUS ID: 2-s2.0-0019415416 04/01/1981       36 Citations
  • Neutropenia in a patient with type IB glycogen storage disease: in vitro response to lithium chloride. (McCabe ER, Melvin TR, O'Brien D, Montgomery RR, Robinson WA, Bhasker C, Brown BI) J Pediatr 1980 Dec;97(6):944-6 PMID: 6255121 SCOPUS ID: 2-s2.0-0019170309 12/01/1980       30 Citations
  • Regression on oxymetholone-induced hepatic tumors after bone marrow transplantation in aplastic anemia. (Montgomery RR, Ducore JM, Githens JH, August CS, Johnson ML) Transplantation 1980 Aug;30(2):90-6 PMID: 7010713 SCOPUS ID: 2-s2.0-0018821928 08/01/1980       15 Citations
  • Acute bleeding emergencies. (Montgomery RR, Hathaway WE) Pediatr Clin North Am 1980 May;27(2):327-44 PMID: 6770325 SCOPUS ID: 2-s2.0-0018836379 05/01/1980    
  • Activated partial thromboplastin time and minor coagulopathies. (Hathaway WE, Assmus SL, Montgomery RR, Dubansky AS) Am J Clin Pathol 1979 Jan;71(1):22-5 PMID: 420168 SCOPUS ID: 2-s2.0-0018394956 01/01/1979       29 Citations
  • Platelet factor VIII-related antigen: immunofluorescent localization. (Slot JW, Bouma BN, Montgomery R, Zimmerman TS) Thromb Res 1978 Nov;13(5):871-81 PMID: 84410 SCOPUS ID: 2-s2.0-0018176922 11/01/1978       30 Citations
  • von Willebrand's disease antigen II. A new plasma and platelet antigen deficient in severe von Willebrand's disease. (Montgomery RR, Zimmerman TS) J Clin Invest 1978 Jun;61(6):1498-507 PMID: 307007 PMCID: PMC372676 SCOPUS ID: 2-s2.0-0017889090 06/01/1978       98 Citations
  • Hypoprothrombinemia: case report. (Montgomery RR, Otsuka A, Hathaway WE) Blood 1978 Feb;51(2):299-306 PMID: 620085 SCOPUS ID: 2-s2.0-0017798727 02/01/1978       10 Citations
  • Regression of oxymetholone induced hepatic tumors following allogeneic bone marrow transplantation for idiopathic acquired aplastic anemia (IAAA) (Montgomery RR, Ducore JM, Githens JH, August CS) Pediatric Research 1977;11(4) SCOPUS ID: 2-s2.0-0017327657 01/01/1977    
  • Clinical and physiologic studies of two siblings with prekallikrein (Fletcher factor) deficiency. (Hathaway WE, Wuepper KD, Weston WL, Humbert JR, Rivers RP, Genton E, August CS, Montgomery RR, Mass MF) Am J Med 1976 May 10;60(5):654-64 PMID: 1020754 SCOPUS ID: 2-s2.0-0017116424 05/10/1976       27 Citations
  • Clinical and physiologic studies of two siblings with prekallikrein (Fletcher factor) deficiency (Hathaway WE, Wuepper KD, Weston WL, Humbert JR, Rivers RPA, Genton E, August CS, Montgomery RR, Mass MF) American Journal of Medicine 1976;60(5):654-664 SCOPUS ID: 2-s2.0-84886604129 01/01/1976       12 Citations
  • A useful test for intracranial hemorrhage (Montgomery RR) The Journal of Pediatrics July 1975;87(1):155 SCOPUS ID: 2-s2.0-0016707057 01/01/1975    
  • Treatment of hemolytic uremic syndrome: role of aspirin and dipyridamole (Montgomery RR, Arenson EB, August CS) Clinical Research 1975;23(2) SCOPUS ID: 2-s2.0-0016425309 01/01/1975    
    • Last update: 08/08/2024